50-198-1643

SGSH/Sulphamidase Rabbit anti-Human, Polyclonal, Bioss

Manufacturer: Bioss

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Pack Size SKU Availability Price
Each of 1 50-198-1643-Each-of-1 In Stock ₹ 36,897.75

50-198-1643 - Each of 1

₹ 36,897.75

In Stock

Quantity

1

Base Price: ₹ 36,897.75

GST (18%): ₹ 6,641.595

Total Price: ₹ 43,539.345

Antigen

SGSH/Sulphamidase

Classification

Polyclonal

Conjugate

Unconjugated

Gene

SGSH

Gene Alias

4632406A19Rik; heparan sulfate sulfatase; HSS; MPS3A; mucopolysaccharidosis type IIIA; N-sulfoglucosamine sulfohydrolase; N-sulfoglucosamine sulfohydrolase (sulfamidase); N-sulphoglucosamine sulphohydrolase; SFMD; SGSH; Sulfoglucosamine sulfamidase; Sulphamidase

Host Species

Rabbit

Purification Method

Protein A

Regulatory Status

RUO

Gene ID (Entrez)

6448

Content And Storage

-20°C

Form

Liquid

Applications

Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration

1 μg/mL

Formulation

PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.

P51688

Gene Symbols

SGSH

Immunogen

KLH conjugated synthetic peptide derived from human Sulphamidase.

Quantity

100 μL

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Isotype

IgG

Description

  • Description SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate
  • Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate
  • Transcripts of varying sizes have been reported but their biological validity has not been determined.

Compare Similar Items

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Bioss

50-198-1643

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Antigen:
SGSH/Sulphamidase

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
SGSH

Gene Alias:
4632406A19Rik; heparan sulfate sulfatase; HSS; MPS3A; mucopolysaccharidosis type IIIA; N-sulfoglucosamine sulfohydrolase; N-sulfoglucosamine sulfohydrolase (sulfamidase); N-sulphoglucosamine sulphohydrolase; SFMD; SGSH; Sulfoglucosamine sulfamidase; Sulphamidase

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
6448

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
P51688

Gene Symbols:
SGSH

Immunogen:
KLH conjugated synthetic peptide derived from human Sulphamidase.

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Bioss

50-198-1645

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Antigen:
SPG3A/Atlastin

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
ATL1

Gene Alias:
4930435M24Rik; Adfsp; AD-FSP; ATL1; ATL1 alpha; ATL1 beta; ATL1 gamma; ATL1-delta; atlastin GTPase 1; atlastin1; Atlastin-1; Bcl11B; BCL-11B; BCL11B/TRDC fusion; Brain-specific GTP-binding protein; Ctip 2; CTIP2; CTIP-2; Fsp1; GBP3; GBP-3; GTP-binding protein 3; Guanine nucleotide-binding protein 3; guanylate-binding protein 3; hGBP3; hRit1; hRIT1 alpha; HSN1D; Rit 1; Rit1; Spastic paraplegia 3 protein A; Spastic paraplegia 3A homolog; Spg3; Spg3a; ZNF856B

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
51062

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
Q8WXF7

Gene Symbols:
ATL1

Immunogen:
KLH conjugated synthetic peptide derived from human SPG3A/Atlastin.

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Bioss

50-198-1647

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Antigen:
SPG48

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
AP5Z1

Gene Alias:
adapter-related protein complex 5 zeta subunit; adaptor related protein complex 5 zeta 1 subunit; adaptor related protein complex 5, zeta 1 subunit; Adaptor-related protein complex 5 zeta subunit; adaptor-related protein complex 5, zeta 1 subunit; AP-5 complex subunit zeta-1; AP5Z1; KIAA0415; protein KIAA0415; SPG48; zeta; Zeta5

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
9907

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
O43299

Gene Symbols:
AP5Z1

Immunogen:
KLH conjugated synthetic peptide derived from human SPG48 .

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Bioss

50-198-1648

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Antigen:
SULT4A1

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
SULT4A1

Gene Alias:
2400007A17Rik; AI853543; BOS_6206; brain sulfotransferase 4A1; Brain sulfotransferase-like protein; BRSTL1; BR-STL-1; DJ388M5.3; hBR-STL; hBR-STL-1; mBR-STL; nervous system cytosolic sulfotransferase; Nervous system sulfotransferase; NST; rBR-STL; ST4A1; Sulfotransferase 4A1; sulfotransferase family 4A member 1; sulfotransferase family 4A, member 1; sulfotransferase-related protein; SULT4A1; SULTX3; Unknown (protein for MGC:136828); zgc:136828

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
25830

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
Q9BR01

Gene Symbols:
SULT4A1

Immunogen:
KLH conjugated synthetic peptide derived from human SULT4A1.

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG