50-198-2743
GAA Rabbit anti-Human, Polyclonal, Bioss
Manufacturer: Bioss
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| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | 50-198-2743-Each-of-1 | In Stock | ₹ 36,897.75 |
50-198-2743 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 36,897.75
GST (18%): ₹ 6,641.595
Total Price: ₹ 43,539.345
Antigen
GAA
Classification
Polyclonal
Conjugate
Unconjugated
Gene
Gaa
Gene Alias
70 kDa lysosomal alpha-glucosidase; 76 kDa lysosomal alpha-glucosidase; acid (Pompe disease, glycogen storage disease type II); acid alpha-glucosidase; Acid maltase; Aglucosidase alfa; E430018M07Rik; Gaa; glucosidase alpha, acid; glucosidase, alpha, acid; glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II); LYAG; Lysosomal alpha-glucosidase
Host Species
Rabbit
Purification Method
Protein A
Regulatory Status
RUO
Gene ID (Entrez)
2548
Content And Storage
-20°C
Form
Liquid
Applications
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration
1 μg/mL
Formulation
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.
P10253
Gene Symbols
Gaa
Immunogen
KLH conjugated synthetic peptide derived from human GAA/Glucosidase alpha.
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human
Product Type
Antibody
Isotype
IgG
Related Products
Description
- This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes
- Different forms of acid alpha-glucosidase are obtained by proteolytic processing
- Defects in this gene are the cause of glycogen storage disease II, also known as Pompe′s disease, which is an autosomal recessive disorder with a broad clinical spectrum
- Three transcript variants encoding the same protein have been found for this gene.
Compare Similar Items
Show Difference
Antigen: GAA
Classification: Polyclonal
Conjugate: Unconjugated
Gene: Gaa
Gene Alias: 70 kDa lysosomal alpha-glucosidase; 76 kDa lysosomal alpha-glucosidase; acid (Pompe disease, glycogen storage disease type II); acid alpha-glucosidase; Acid maltase; Aglucosidase alfa; E430018M07Rik; Gaa; glucosidase alpha, acid; glucosidase, alpha, acid; glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II); LYAG; Lysosomal alpha-glucosidase
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 2548
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: P10253
Gene Symbols: Gaa
Immunogen: KLH conjugated synthetic peptide derived from human GAA/Glucosidase alpha.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
GAA
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
Gaa
Gene Alias:
70 kDa lysosomal alpha-glucosidase; 76 kDa lysosomal alpha-glucosidase; acid (Pompe disease, glycogen storage disease type II); acid alpha-glucosidase; Acid maltase; Aglucosidase alfa; E430018M07Rik; Gaa; glucosidase alpha, acid; glucosidase, alpha, acid; glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II); LYAG; Lysosomal alpha-glucosidase
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
2548
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
P10253
Gene Symbols:
Gaa
Immunogen:
KLH conjugated synthetic peptide derived from human GAA/Glucosidase alpha.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: GAB3
Classification: Polyclonal
Conjugate: Unconjugated
Gene: GAB3
Gene Alias: 5930433H21Rik; DOS/Gab family member 3; GAB3; Gab3 scaffolding protein; GRB2 associated binding protein 3; GRB2-associated binder 3; GRB2-associated binding protein 3; GRB2-associated-binding protein 3; Growth factor receptor bound protein 2-associated protein 3
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 139716
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: Q8WWW8
Gene Symbols: GAB3
Immunogen: KLH conjugated synthetic peptide derived from human GAB3.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
GAB3
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
GAB3
Gene Alias:
5930433H21Rik; DOS/Gab family member 3; GAB3; Gab3 scaffolding protein; GRB2 associated binding protein 3; GRB2-associated binder 3; GRB2-associated binding protein 3; GRB2-associated-binding protein 3; Growth factor receptor bound protein 2-associated protein 3
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
139716
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
Q8WWW8
Gene Symbols:
GAB3
Immunogen:
KLH conjugated synthetic peptide derived from human GAB3.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: GAB4
Classification: Polyclonal
Conjugate: Unconjugated
Gene: GAB4
Gene Alias: GAB2-like; GAB4; GRB2 associated binding protein family member 4; GRB2-associated binder 2-like; GRB2-associated binder 2-like protein; GRB2-associated binder 4; GRB2-associated binding protein family, member 4; GRB2-associated-binding protein 2-like; GRB2-associated-binding protein 4; Growth factor receptor bound protein 2-associated protein 4
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 128954
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: Q2WGN9
Gene Symbols: GAB4
Immunogen: KLH conjugated synthetic peptide derived from human GAB4.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
GAB4
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
GAB4
Gene Alias:
GAB2-like; GAB4; GRB2 associated binding protein family member 4; GRB2-associated binder 2-like; GRB2-associated binder 2-like protein; GRB2-associated binder 4; GRB2-associated binding protein family, member 4; GRB2-associated-binding protein 2-like; GRB2-associated-binding protein 4; Growth factor receptor bound protein 2-associated protein 4
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
128954
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
Q2WGN9
Gene Symbols:
GAB4
Immunogen:
KLH conjugated synthetic peptide derived from human GAB4.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: GABRP/GABA A receptor pi
Classification: Polyclonal
Conjugate: Unconjugated
Gene: GABRP
Gene Alias: GABA(A) receptor subunit pi; GABA(A) receptor, pi; GABA-A receptor pi subunit; GABRP; gamma-aminobutyric acid (GABA) A receptor, pi; gamma-aminobutyric acid (GABA-A) receptor, pi; gamma-aminobutyric acid A receptor, pi; Gamma-aminobutyric acid receptor subunit pi; gamma-aminobutyric acid type A receptor pi subunit; MGC126386; MGC126387
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 2568
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: O00591
Gene Symbols: GABRP
Immunogen: KLH conjugated synthetic peptide derived from human GABRP/GABA A receptor pi.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
GABRP/GABA A receptor pi
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
GABRP
Gene Alias:
GABA(A) receptor subunit pi; GABA(A) receptor, pi; GABA-A receptor pi subunit; GABRP; gamma-aminobutyric acid (GABA) A receptor, pi; gamma-aminobutyric acid (GABA-A) receptor, pi; gamma-aminobutyric acid A receptor, pi; Gamma-aminobutyric acid receptor subunit pi; gamma-aminobutyric acid type A receptor pi subunit; MGC126386; MGC126387
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
2568
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
O00591
Gene Symbols:
GABRP
Immunogen:
KLH conjugated synthetic peptide derived from human GABRP/GABA A receptor pi.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG