50-198-3796
HEXB chain B Rabbit anti-Human, Polyclonal, Bioss
Manufacturer: Bioss
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| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | 50-198-3796-Each-of-1 | In Stock | ₹ 36,897.75 |
50-198-3796 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 36,897.75
GST (18%): ₹ 6,641.595
Total Price: ₹ 43,539.345
Antigen
HEXB chain B
Classification
Polyclonal
Conjugate
Unconjugated
Gene
Hexb
Gene Alias
Beta-hexosaminidase subunit beta; Beta-hexosaminidase subunit beta chain A; Beta-hexosaminidase subunit beta chain B; Beta-N-acetylhexosaminidase subunit beta; Cervical cancer proto-oncogene 7 protein; ENC-1AS; epididymis luminal protein 248; epididymis secretory protein Li 111; HCC7; HCC-7; HEL-248; HEL-S-111; Hexb; hexosaminidase B; hexosaminidase B (beta polypeptide); Hexosaminidase subunit B; hexosaminidase subunit beta; N-acetyl-beta-glucosaminidase subunit beta
Host Species
Rabbit
Purification Method
Protein A
Regulatory Status
RUO
Gene ID (Entrez)
3074
Content And Storage
-20°C
Form
Liquid
Applications
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration
1 μg/mL
Formulation
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.
P07686
Gene Symbols
Hexb
Immunogen
KLH conjugated synthetic peptide derived from human HEXB chain B.
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human
Product Type
Antibody
Isotype
IgG
Related Products
Description
- Hexosaminidase B (HEXB), also designated beta-hexosaminidase B, is a Hexosaminidase B (HEXB), also designated b-hexosaminidase B, is a tetramer of two b-A and two b-B chains and is found in the lysosomes of cells
- Sandhoff disease (SD), also known as GM2-gangliosidosis type II, is caused by mutations in the HEXB gene that affect the b subunit
- These mutations disrupt the activity of HEXB and HEXA, which prevents the breakdown of GM2 ganglioside, a fatty material found in the brain, therby rendering both the HEXA and HEXB enzymes deficient
- SD is a rare autosomal recessive disorder characterized by an accumulation of GM2 ganglioside, which causes progressive destruction of the central nervous system
- Sandhoff disease is similar to Tay-Sachs disease, which is caused by mutations in the HEXA gene, although SD is more severe.
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Antigen: HEXB chain B
Classification: Polyclonal
Conjugate: Unconjugated
Gene: Hexb
Gene Alias: Beta-hexosaminidase subunit beta; Beta-hexosaminidase subunit beta chain A; Beta-hexosaminidase subunit beta chain B; Beta-N-acetylhexosaminidase subunit beta; Cervical cancer proto-oncogene 7 protein; ENC-1AS; epididymis luminal protein 248; epididymis secretory protein Li 111; HCC7; HCC-7; HEL-248; HEL-S-111; Hexb; hexosaminidase B; hexosaminidase B (beta polypeptide); Hexosaminidase subunit B; hexosaminidase subunit beta; N-acetyl-beta-glucosaminidase subunit beta
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 3074
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: P07686
Gene Symbols: Hexb
Immunogen: KLH conjugated synthetic peptide derived from human HEXB chain B.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
HEXB chain B
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
Hexb
Gene Alias:
Beta-hexosaminidase subunit beta; Beta-hexosaminidase subunit beta chain A; Beta-hexosaminidase subunit beta chain B; Beta-N-acetylhexosaminidase subunit beta; Cervical cancer proto-oncogene 7 protein; ENC-1AS; epididymis luminal protein 248; epididymis secretory protein Li 111; HCC7; HCC-7; HEL-248; HEL-S-111; Hexb; hexosaminidase B; hexosaminidase B (beta polypeptide); Hexosaminidase subunit B; hexosaminidase subunit beta; N-acetyl-beta-glucosaminidase subunit beta
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
3074
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
P07686
Gene Symbols:
Hexb
Immunogen:
KLH conjugated synthetic peptide derived from human HEXB chain B.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: HEXIM2
Classification: Polyclonal
Conjugate: Unconjugated
Gene: HEXIM2
Gene Alias: 4933402L21Rik; hexamethylene bisacetamide inducible 2; hexamethylene bis-acetamide inducible 2; Hexamethylene bis-acetamide-inducible protein 2; hexamethylene-bis-acetamide-inducible transcript 2; hexamthylene bis-acetamide inducible 2; HEXIM2; L3; MAQ1 paralog; Protein HEXIM2; RGD1311635
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 124790
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: Q96MH2
Gene Symbols: HEXIM2
Immunogen: KLH conjugated synthetic peptide derived from human HEXIM2.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
HEXIM2
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
HEXIM2
Gene Alias:
4933402L21Rik; hexamethylene bisacetamide inducible 2; hexamethylene bis-acetamide inducible 2; Hexamethylene bis-acetamide-inducible protein 2; hexamethylene-bis-acetamide-inducible transcript 2; hexamthylene bis-acetamide inducible 2; HEXIM2; L3; MAQ1 paralog; Protein HEXIM2; RGD1311635
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
124790
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
Q96MH2
Gene Symbols:
HEXIM2
Immunogen:
KLH conjugated synthetic peptide derived from human HEXIM2.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: beta Adaptin/AP2 beta
Classification: Polyclonal
Conjugate: Unconjugated
Gene: GTF3A
Gene Alias: AP2; general transcription factor IIIA; GTF3A; TF3A; TFIIIA; Transcription factor IIIA
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 2971
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: Q92664
Gene Symbols: GTF3A
Immunogen: KLH conjugated synthetic peptide derived from human beta Adaptin.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
beta Adaptin/AP2 beta
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
GTF3A
Gene Alias:
AP2; general transcription factor IIIA; GTF3A; TF3A; TFIIIA; Transcription factor IIIA
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
2971
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
Q92664
Gene Symbols:
GTF3A
Immunogen:
KLH conjugated synthetic peptide derived from human beta Adaptin.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: HGD
Classification: Polyclonal
Conjugate: Unconjugated
Gene: HGD
Gene Alias: Aku; alkaptonuria; HGD; HGO; homogentisate 1, 2-dioxygenase; Homogentisate 1,2-dioxygenase; homogentisate oxidase; Homogentisate oxygenase; Homogentisic acid oxidase; Homogentisicase
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 3081
Content And Storage: -20°C
Form: Liquid
Applications: Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration: 1 μg/mL
Formulation: PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.: Q93099
Gene Symbols: HGD
Immunogen: KLH conjugated synthetic peptide derived from human HGD.
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
HGD
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
HGD
Gene Alias:
Aku; alkaptonuria; HGD; HGO; homogentisate 1, 2-dioxygenase; Homogentisate 1,2-dioxygenase; homogentisate oxidase; Homogentisate oxygenase; Homogentisic acid oxidase; Homogentisicase
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
3081
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
Concentration:
1 μg/mL
Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH
Gene Accession No.:
Q93099
Gene Symbols:
HGD
Immunogen:
KLH conjugated synthetic peptide derived from human HGD.
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG