50-198-8202

CLN3 Rabbit anti-Human, Polyclonal, Bioss

Manufacturer: Bioss

Select a Size

Pack Size SKU Availability Price
Each of 1 50-198-8202-Each-of-1 In Stock ₹ 36,897.75

50-198-8202 - Each of 1

₹ 36,897.75

In Stock

Quantity

1

Base Price: ₹ 36,897.75

GST (18%): ₹ 6,641.595

Total Price: ₹ 43,539.345

Antigen

CLN3

Classification

Polyclonal

Conjugate

Unconjugated

Gene

CLN3

Gene Alias

AI323623; Batten disease protein; Battenin; BTS; ceroid lipofuscinosis, neuronal 3, juvenile (Batten, Spielmeyer-Vogt disease); ceroid-lipofuscinosis, neuronal 3; CLN 3; Cln3; CLN3, battenin; Cln3p; JNCL; MGC102840; Protein CLN3

Host Species

Rabbit

Purification Method

Protein A

Regulatory Status

RUO

Gene ID (Entrez)

1201

Content And Storage

-20°C

Form

Liquid

Applications

Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration

1 μg/mL

Formulation

PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.

Q13286

Gene Symbols

CLN3

Immunogen

KLH conjugated synthetic peptide derived from human CLN3.

Quantity

100 μL

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Isotype

IgG

Related Products

Img

Bioss

50-198-1608

--

Img

Bioss

50-198-8114

--

Img

Bioss

50-198-6058

--

Img

Bioss

50-198-8186

--

Img

Bioss

50-198-8095

--

Img

Bioss

50-198-5977

--

Img

Bioss

50-198-8074

--

Img

Bioss

50-198-8307

--

Description

  • CLN3 is a highly glycosylated, hydrophobic, 438-amino acid protein with 6 transmembrane domains
  • The CLN3 protein localizes to the lysosomal membrane and plays a role in lysosomal function
  • It may act as a chaperone involved in the folding and unfolding of other proteins, namely subunit C of the ATP synthase complex
  • Mutations in the CLN3 gene cause Batten disease, a recessively inherited neurodegenerative disorder of childhood caused by lysosomal accumulation of hydrophobic material, mainly ATP synthase subunit C
  • Batten disease is the most common form of a group of disorders known as neuronal ceroid lipofuscinoses (NCLs)
  • Symptoms of Batten disease include progressive loss of vision, seizures, and psychomotor disturbances.

Compare Similar Items

Show Difference

Img

Bioss

50-198-8202

--


Antigen:
CLN3

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
CLN3

Gene Alias:
AI323623; Batten disease protein; Battenin; BTS; ceroid lipofuscinosis, neuronal 3, juvenile (Batten, Spielmeyer-Vogt disease); ceroid-lipofuscinosis, neuronal 3; CLN 3; Cln3; CLN3, battenin; Cln3p; JNCL; MGC102840; Protein CLN3

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
1201

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
Q13286

Gene Symbols:
CLN3

Immunogen:
KLH conjugated synthetic peptide derived from human CLN3.

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Bioss

50-198-8203

--


Antigen:
CLN6

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
CLN6

Gene Alias:
1810065L06Rik; AW743417; ceroid-lipofuscinosis neuronal 6 late infantile; Ceroid-lipofuscinosis neuronal protein 6; ceroid-lipofuscinosis, neuronal 6; ceroid-lipofuscinosis, neuronal 6, late infantile, variant; CLN4A; CLN6; D9Bwg1455e; HsT18960; nclf; neuronal ceroid lipofuscinosis; Protein CLN6

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
54982

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
Q9NWW5

Gene Symbols:
CLN6

Immunogen:
KLH conjugated synthetic peptide derived from human CLN6.

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Bioss

50-198-8204

--


Antigen:
CLPTM1

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
CLPTM1

Gene Alias:
cleft lip and palate associated transmembrane protein 1; Cleft lip and palate transmembrane protein 1; Cleft lip and palate transmembrane protein 1 homolog; CLPTM1; CLPTM1, transmembrane protein; HS9; N14; Thymic epithelial cell surface antigen

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
1209

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
O96005

Gene Symbols:
CLPTM1

Immunogen:
KLH conjugated synthetic peptide derived from human CLPTM1.

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Bioss

50-198-8207

--


Antigen:
CKLFH3

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
CMTM3

Gene Alias:
BNAS2; Chemokine-like factor superfamily member 3; CKLF like MARVEL transmembrane domain containing 3; CKLF-like MARVEL transmembrane domain containing 3; CKLF-like MARVEL transmembrane domain-containing protein 3; CKLFSF3; CMTM3

Host Species:
Rabbit

Purification Method:
Protein A

Regulatory Status:
RUO

Gene ID (Entrez):
123920

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 μg/mL

Formulation:
PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.:
Q96MX0

Gene Symbols:
CMTM3

Immunogen:
KLH conjugated synthetic peptide derived from human CKLFH3/CMTM3.

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG