50-559-933
HEXB Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech
Manufacturer: Proteintech Group Inc
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| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | 50-559-933-Each-of-1 | In Stock | ₹ 44,150.23 |
50-559-933 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 44,150.23
GST (18%): ₹ 7,947.041
Total Price: ₹ 52,097.271
Antigen
HEXB
Classification
Polyclonal
Conjugate
Unconjugated
Gene
HEXB
Gene Alias
ENC 1AS, HCC 7, HEXB, Hexosaminidase subunit B
Host Species
Rabbit
Purification Method
Antigen Affinity Chromatography
Regulatory Status
RUO
Gene ID (Entrez)
15212, 294673, 3074
Content And Storage
-20°C
Form
Liquid
Applications
Immunohistochemistry (Paraffin), Western Blot
Concentration
0.35 mg/mL
Formulation
PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Accession No.
P07686, P20060, Q6AXR4
Gene Symbols
Hexb
Immunogen
HEXB Fusion Protein Ag8683
Quantity
150 μL
Primary or Secondary
Primary
Target Species
Human, Mouse, Rat
Product Type
Antibody
Isotype
IgG
Related Products
Description
- Hexosaminidase B (HEXB), also designated beta-hexosaminidase B, is a Hexosaminidase B (HEXB), also designated b-hexosaminidase B, is a tetramer of two b-A and two b-B chains and is found in the lysosomes of cells
- Sandhoff disease (SD), also known as GM2-gangliosidosis type II, is caused by mutations in the HEXB gene that affect the b subunit
- These mutations disrupt the activity of HEXB and HEXA, which prevents the breakdown of GM2 ganglioside, a fatty material found in the brain, therby rendering both the HEXA and HEXB enzymes deficient
- SD is a rare autosomal recessive disorder characterized by an accumulation of GM2 ganglioside, which causes progressive destruction of the central nervous system
- Sandhoff disease is similar to Tay-Sachs disease, which is caused by mutations in the HEXA gene, although SD is more severe.
Compare Similar Items
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Antigen: HEXB
Classification: Polyclonal
Conjugate: Unconjugated
Gene: HEXB
Gene Alias: ENC 1AS, HCC 7, HEXB, Hexosaminidase subunit B
Host Species: Rabbit
Purification Method: Antigen Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 15212, 294673, 3074
Content And Storage: -20°C
Form: Liquid
Applications: Immunohistochemistry (Paraffin), Western Blot
Concentration: 0.35 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Accession No.: P07686, P20060, Q6AXR4
Gene Symbols: Hexb
Immunogen: HEXB Fusion Protein Ag8683
Quantity: 150 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
HEXB
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
HEXB
Gene Alias:
ENC 1AS, HCC 7, HEXB, Hexosaminidase subunit B
Host Species:
Rabbit
Purification Method:
Antigen Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
15212, 294673, 3074
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunohistochemistry (Paraffin), Western Blot
Concentration:
0.35 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Accession No.:
P07686, P20060, Q6AXR4
Gene Symbols:
Hexb
Immunogen:
HEXB Fusion Protein Ag8683
Quantity:
150 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG
Antigen: MYL7
Classification: Polyclonal
Conjugate: Unconjugated
Gene: MYL7
Gene Alias: MLC 2a, MLC2a, MYL2A, MYL7, MYLC2A, Myosin light chain 2a
Host Species: Rabbit
Purification Method: Antigen Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 17898, 289759, 58498
Content And Storage: -20°C
Form: Liquid
Applications: Immunocytochemistry, Immunofluorescence, Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot
Concentration: 0.36 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Accession No.: Q01449, Q9QVP4
Gene Symbols: Myl7
Immunogen: MYL7 Fusion Protein Ag11058
Quantity: 150 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
MYL7
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
MYL7
Gene Alias:
MLC 2a, MLC2a, MYL2A, MYL7, MYLC2A, Myosin light chain 2a
Host Species:
Rabbit
Purification Method:
Antigen Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
17898, 289759, 58498
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunocytochemistry, Immunofluorescence, Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot
Concentration:
0.36 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Accession No.:
Q01449, Q9QVP4
Gene Symbols:
Myl7
Immunogen:
MYL7 Fusion Protein Ag11058
Quantity:
150 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG
Antigen: LGR6
Classification: Polyclonal
Conjugate: Unconjugated
Gene: LGR6
Gene Alias: GPCR, LGR6, VTS20631
Host Species: Rabbit
Purification Method: Antigen Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 329252, 498233, 59352
Content And Storage: -20°C
Form: Liquid
Applications: Flow Cytometry, Immunohistochemistry (Paraffin), Western Blot
Concentration: 0.13 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Accession No.: Q3UVD5, Q9HBX8
Gene Symbols: Lgr6
Immunogen: LGR6 Fusion Protein Ag11909
Quantity: 150 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
LGR6
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
LGR6
Gene Alias:
GPCR, LGR6, VTS20631
Host Species:
Rabbit
Purification Method:
Antigen Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
329252, 498233, 59352
Content And Storage:
-20°C
Form:
Liquid
Applications:
Flow Cytometry, Immunohistochemistry (Paraffin), Western Blot
Concentration:
0.13 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Accession No.:
Q3UVD5, Q9HBX8
Gene Symbols:
Lgr6
Immunogen:
LGR6 Fusion Protein Ag11909
Quantity:
150 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG
Antigen: JTV1
Classification: Polyclonal
Conjugate: Unconjugated
Gene: AIMP2
Gene Alias: AIMP2, JTV1, JTV1 gene, P38, PRO0992, Protein JTV 1
Host Species: Rabbit
Purification Method: Antigen Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 231872, 288480, 7965
Content And Storage: -20°C
Form: Liquid
Applications: Immunocytochemistry, Immunofluorescence, Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot
Concentration: 0.35 mg/mL
Formulation: PBS with 50% glycerol and 0.1% sodium azide; pH 7.3
Gene Accession No.: Q13155, Q32PX2, Q8R010
Gene Symbols: Aimp2
Immunogen: JTV1 Fusion Protein Ag0675
Quantity: 150 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
JTV1
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
AIMP2
Gene Alias:
AIMP2, JTV1, JTV1 gene, P38, PRO0992, Protein JTV 1
Host Species:
Rabbit
Purification Method:
Antigen Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
231872, 288480, 7965
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunocytochemistry, Immunofluorescence, Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot
Concentration:
0.35 mg/mL
Formulation:
PBS with 50% glycerol and 0.1% sodium azide; pH 7.3
Gene Accession No.:
Q13155, Q32PX2, Q8R010
Gene Symbols:
Aimp2
Immunogen:
JTV1 Fusion Protein Ag0675
Quantity:
150 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG