89-017-653

glucosidase, alpha; acid, Rabbit, Purified MaxPab™ Polyclonal Antibody, Abnova™

Manufacturer: Abnova Corporation

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Pack Size SKU Availability Price
Each of 1 89-017-653-Each-of-1 In Stock ₹ 53,988.36

89-017-653 - Each of 1

₹ 53,988.36

In Stock

Quantity

1

Base Price: ₹ 53,988.36

GST (18%): ₹ 9,717.905

Total Price: ₹ 63,706.265

Antigen

glucosidase, alpha; acid

Classification

Polyclonal

Description

Rabbit polyclonal antibody raised against a full-length human GAA protein.

Gene

GAA

Gene Alias

LYAG

Host Species

Rabbit

Purification Method

Affinity Purified

Regulatory Status

RUO

Gene ID (Entrez)

2548

Content And Storage

Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

Isotype

IgG

Applications

Western Blot

Conjugate

Unconjugated

Formulation

PBS with no preservative; pH 7.4

Gene Accession No.

NM_000152.2

Gene Symbols

GAA

Immunogen

GAA (P10253, 1 a.a. ∼ 952 a.a) full-length human protein.

Quantity

100 μg

Primary or Secondary

Primary

Target Species

Human, Mouse

Product Type

Antibody

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Description

  • This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes
  • Different forms of acid alpha-glucosidase are obtained by proteolytic processing
  • Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum
  • Three transcript variants encoding the same protein have been found for this gene
  • [provided by RefSeq] Sequence: MGVRHPPCSHRLLAVCALVSLATAALLGHILLHDFLLVPRELSGSSPVLEETHPAHQQGASRPGPRDAQAHPGRPRAVPTQCDVPPNSRFDCAPDKAITQEQCEARGCCYIPAKQGLQGAQMGQPWCFFPPSYPSYKLENLSSSEMGYTATLTRTTPTFFPKDILTLRLDVMMETENRLHFTIKDPANRRYEVPLETPRVHSRAPSPLYSVEFSEEPFGVIVHRQLDGRVLLNTTVAPLFFADQFLQLSTSLPSQYITGLAEHLSPLMLSTSWTRITLWNRDLAPTPGANLYGSHPFYLALEDGGSAHGVFLLNSNAMDVVLQPSPALSWRSTGGILDVYIFLGPEPKSVVQQYLDVVGYPFMPPYWGLGFHLCRWGYSSTAITRQVVENMTRAHFPLDVQWNDLDYMDSRRDFTFNKDGFRDFPAMVQELHQGGRRYMMIVDPAISSSGPAGSYRPYDEGLRRGVFITNETGQPLIGKVWPGSTAFPDFTNPTALAWWEDMVAEFHDQVPFDGMWIDMNEPSNFIRGSEDGCPNNELENPPYVPGVVGGTLQAATICASSHQFLSTHYNLHNLYGLTEAIASHRALVKARGTRPFVISRSTFAGHGRYAGHWTGDVWSSWEQLASSVPEILQFNLLGVPLVGADVCGFLGNTSEELCVRWTQLGAFYPFMRNHNSLLSLPQEPYSFSEPAQQAMRKALTLRYALLPHLYTLFHQAHVAGETVARPLFLEFPKDSSTWTVDHQLLWGEALLITPVLQAGKAEVTGYFPLGTWYDLQTVPIEALGSLPPPPAAPREPAIHSEGQWVTLPAPLDTINVHLRAGYIIPLQGPGLTTTESRQQPMALAVALTKGGEARGELFWDDGESLEVLERGAYTQVIFLARNNTIVNELVRVTSEGAGLQLQKVTVLGVATAPQQVLSNGVPVSNFTYSPDTKVLDICVSLLMGEQFLVSWC

Compare Similar Items

Show Difference

Img

Abnova Corporation

89-017-653

--


Antigen:
glucosidase, alpha; acid

Classification:
Polyclonal

Description:
Rabbit polyclonal antibody raised against a full-length human GAA protein.

Gene:
GAA

Gene Alias:
LYAG

Host Species:
Rabbit

Purification Method:
Affinity Purified

Regulatory Status:
RUO

Gene ID (Entrez):
2548

Content And Storage:
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

Isotype:
IgG

Applications:
Western Blot

Conjugate:
Unconjugated

Formulation:
PBS with no preservative; pH 7.4

Gene Accession No.:
NM_000152.2

Gene Symbols:
GAA

Immunogen:
GAA (P10253, 1 a.a. ∼ 952 a.a) full-length human protein.

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human, Mouse

Product Type:
Antibody

Img

Abnova Corporation

89-017-654

--


Antigen:
GRB2-associated binding protein 1

Classification:
Polyclonal

Description:
Rabbit polyclonal antibody raised against a full-length human GAB1 protein.

Gene:
GAB1

Gene Alias:
__

Host Species:
Rabbit

Purification Method:
Affinity Purified

Regulatory Status:
RUO

Gene ID (Entrez):
2549

Content And Storage:
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

Isotype:
__

Applications:
In situ PLA, Western Blot

Conjugate:
Unconjugated

Formulation:
In 1X PBS, pH 7.4

Gene Accession No.:
NM_207123

Gene Symbols:
GAB1

Immunogen:
GAB1 (NP_997006.1, 1 a.a. ∼ 724 a.a) full-length human protein.

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
__

Img

Abnova Corporation

89-017-655

--


Antigen:
GA binding protein transcription factor, alpha subunit 60kDa

Classification:
Polyclonal

Description:
Rabbit polyclonal antibody raised against a full-length human GABPA protein.

Gene:
GABPA

Gene Alias:
E4TF1-60/E4TF1A/NFT2/NRF2/NRF2A

Host Species:
Rabbit

Purification Method:
Affinity Purified

Regulatory Status:
RUO

Gene ID (Entrez):
2551

Content And Storage:
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

Isotype:
IgG

Applications:
Western Blot

Conjugate:
Unconjugated

Formulation:
PBS with no preservative; pH 7.4

Gene Accession No.:
BC035031.2

Gene Symbols:
GABPA

Immunogen:
GABPA (AAH35031.1, 1 a.a. ∼ 454 a.a) full-length human protein.

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Img

Abnova Corporation

89-017-656

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Antigen:
glutamate decarboxylase 1 (brain, 67kDa)

Classification:
Polyclonal

Description:
Rabbit polyclonal antibody raised against a full-length human GAD1 protein.

Gene:
GAD1

Gene Alias:
FLJ45882/GAD/SCP

Host Species:
Rabbit

Purification Method:
Affinity Purified

Regulatory Status:
RUO

Gene ID (Entrez):
2571

Content And Storage:
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

Isotype:
IgG

Applications:
Western Blot

Conjugate:
Unconjugated

Formulation:
PBS with no preservative; pH 7.4

Gene Accession No.:
NM_000817.2

Gene Symbols:
GAD1

Immunogen:
GAD1 (NP_000808.2, 1 a.a. ∼ 594 a.a) full-length human protein.

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody