PA551347
Dysferlin Polyclonal Antibody, Invitrogen™
Manufacturer: Thermo Scientific
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| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | PA551347-Each-of-1 | In Stock | ₹ 46,245.18 |
PA551347 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 46,245.18
GST (18%): ₹ 8,324.132
Total Price: ₹ 54,569.312
Antigen
Dysferlin
Classification
Polyclonal
Conjugate
Unconjugated
Gene
DYSF
Gene Alias
2310004N10Rik; AI604795; D6Pas3; Dysf; Dysferlin; dysferlin variant a; dysferlin_a; dystrophy-associated fer-1-like 1; dystrophy-associated fer-1-like protein; FER1L1; fer-1-like family member 1; fer-1-like protein 1; FLJ00175; FLJ90168; LGMD2B; limb girdle muscular dystrophy 2B (autosomal recessive); MMD1
Host Species
Rabbit
Purification Method
Antigen affinity chromatography
Regulatory Status
RUO
Gene ID (Entrez)
26903, 8291
Content And Storage
-20°C
Form
Liquid
Applications
Immunohistochemistry (Paraffin)
Concentration
1.8 mg/mL
Formulation
PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.
O75923, Q9ESD7
Gene Symbols
DYSF
Immunogen
Synthetic peptide of human DYSF
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human, Mouse
Product Type
Antibody
Isotype
IgG
Related Products
Description
- The antibody detects endogenous levels of total Dysferlin protein
- Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM)
- Dysferlin is normally localized to the muscle plasma membrane
- In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation
- This antibody is used for the characterization of LGMD2B and MM.
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Antigen: Dysferlin
Classification: Polyclonal
Conjugate: Unconjugated
Gene: DYSF
Gene Alias: 2310004N10Rik; AI604795; D6Pas3; Dysf; Dysferlin; dysferlin variant a; dysferlin_a; dystrophy-associated fer-1-like 1; dystrophy-associated fer-1-like protein; FER1L1; fer-1-like family member 1; fer-1-like protein 1; FLJ00175; FLJ90168; LGMD2B; limb girdle muscular dystrophy 2B (autosomal recessive); MMD1
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 26903, 8291
Content And Storage: -20°C
Form: Liquid
Applications: Immunohistochemistry (Paraffin)
Concentration: 1.8 mg/mL
Formulation: PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: O75923, Q9ESD7
Gene Symbols: DYSF
Immunogen: Synthetic peptide of human DYSF
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human, Mouse
Product Type: Antibody
Isotype: IgG
Antigen:
Dysferlin
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
DYSF
Gene Alias:
2310004N10Rik; AI604795; D6Pas3; Dysf; Dysferlin; dysferlin variant a; dysferlin_a; dystrophy-associated fer-1-like 1; dystrophy-associated fer-1-like protein; FER1L1; fer-1-like family member 1; fer-1-like protein 1; FLJ00175; FLJ90168; LGMD2B; limb girdle muscular dystrophy 2B (autosomal recessive); MMD1
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
26903, 8291
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunohistochemistry (Paraffin)
Concentration:
1.8 mg/mL
Formulation:
PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
O75923, Q9ESD7
Gene Symbols:
DYSF
Immunogen:
Synthetic peptide of human DYSF
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse
Product Type:
Antibody
Isotype:
IgG
Antigen: ADAMTS8
Classification: Polyclonal
Conjugate: Unconjugated
Gene: ADAMTS8
Gene Alias: a disintegrin and metalloproteinase; A disintegrin and metalloproteinase with thrombospondin motifs 8; a disintegrin-like and metallopeptidase (reprolysin type) with thrombospondin type 1 motif, 8; a disintegrin-like and metalloprotease (reprolysin type) with thrombospondin type 1 motif, 8; ADAM; ADAM metallopeptidase with thrombospondin type 1 motif 8; ADAM metallopeptidase with thrombospondin type 1 motif, 8; ADAMs; ADAM-TS 8; ADAMTS8; ADAM-TS8; ADAMTS-8; ADAMTS-8 precursor (A disintegrin and metalloproteinase with thrombospondin motifs 8) (ADAM-TS 8) (ADAM-TS8) (METH-2); EC 3.4.24.14; EC 3.4.24.82; FLJ41712; metalloendopeptidases; METH2; METH-2; METH2ADAM-TS METH-8; METH-8
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 11095
Content And Storage: -20°C
Form: Liquid
Applications: Immunohistochemistry (Paraffin)
Concentration: 1.6 mg/mL
Formulation: PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: Q9UP79
Gene Symbols: ADAMTS8
Immunogen: Synthetic peptide of human ADAMTS8
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
ADAMTS8
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
ADAMTS8
Gene Alias:
a disintegrin and metalloproteinase; A disintegrin and metalloproteinase with thrombospondin motifs 8; a disintegrin-like and metallopeptidase (reprolysin type) with thrombospondin type 1 motif, 8; a disintegrin-like and metalloprotease (reprolysin type) with thrombospondin type 1 motif, 8; ADAM; ADAM metallopeptidase with thrombospondin type 1 motif 8; ADAM metallopeptidase with thrombospondin type 1 motif, 8; ADAMs; ADAM-TS 8; ADAMTS8; ADAM-TS8; ADAMTS-8; ADAMTS-8 precursor (A disintegrin and metalloproteinase with thrombospondin motifs 8) (ADAM-TS 8) (ADAM-TS8) (METH-2); EC 3.4.24.14; EC 3.4.24.82; FLJ41712; metalloendopeptidases; METH2; METH-2; METH2ADAM-TS METH-8; METH-8
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
11095
Content And Storage:
-20°C
Form:
Liquid
Applications:
Immunohistochemistry (Paraffin)
Concentration:
1.6 mg/mL
Formulation:
PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
Q9UP79
Gene Symbols:
ADAMTS8
Immunogen:
Synthetic peptide of human ADAMTS8
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: SLC4A3
Classification: Polyclonal
Conjugate: Unconjugated
Gene: SLC4A3
Gene Alias: A930038D23Rik; AE 3; Ae3; Aep3; anion exchange protein 3; anion exchanger 3; anion exchanger 3 cardiac isoform; Anion exchanger 3, neuronal; B3rp3; B3RP-3; Band 3-related protein 3; CAE3/BAE3; Cardiac/brain band 3-like protein; neuronal band 3-like protein; SLC2C; Slc4a3; solute carrier family 4 (anion exchanger), member 3; solute carrier family 4 member 3; Solute carrier family 4, member 3, anion exchange protein 3
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 20536, 24781, 6508
Content And Storage: -20°C
Form: Liquid
Applications: Western Blot
Concentration: 0.9 mg/mL
Formulation: PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: P16283, P23348, P48751
Gene Symbols: SLC4A3
Immunogen: Synthetic peptide of human SLC4A3
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
SLC4A3
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
SLC4A3
Gene Alias:
A930038D23Rik; AE 3; Ae3; Aep3; anion exchange protein 3; anion exchanger 3; anion exchanger 3 cardiac isoform; Anion exchanger 3, neuronal; B3rp3; B3RP-3; Band 3-related protein 3; CAE3/BAE3; Cardiac/brain band 3-like protein; neuronal band 3-like protein; SLC2C; Slc4a3; solute carrier family 4 (anion exchanger), member 3; solute carrier family 4 member 3; Solute carrier family 4, member 3, anion exchange protein 3
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
20536, 24781, 6508
Content And Storage:
-20°C
Form:
Liquid
Applications:
Western Blot
Concentration:
0.9 mg/mL
Formulation:
PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
P16283, P23348, P48751
Gene Symbols:
SLC4A3
Immunogen:
Synthetic peptide of human SLC4A3
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG
Antigen: NUDT19
Classification: Polyclonal
Conjugate: Unconjugated
Gene: NUDT19
Gene Alias: CTC-379B2.4; nucleoside diphosphate-linked moiety X motif 19; nucleoside diphosphate-linked moiety X motif 19, mitochondrial; nudix (nucleoside diphosphate linked moiety X)-type motif 19; nudix hydrolase 19; nudix motif 19; NUDT19; RP2
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 390916
Content And Storage: -20°C
Form: Liquid
Applications: Western Blot
Concentration: 1.5 mg/mL
Formulation: PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: A8MXV4
Gene Symbols: NUDT19
Immunogen: Synthetic peptide of human NUDT19
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
NUDT19
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
NUDT19
Gene Alias:
CTC-379B2.4; nucleoside diphosphate-linked moiety X motif 19; nucleoside diphosphate-linked moiety X motif 19, mitochondrial; nudix (nucleoside diphosphate linked moiety X)-type motif 19; nudix hydrolase 19; nudix motif 19; NUDT19; RP2
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
390916
Content And Storage:
-20°C
Form:
Liquid
Applications:
Western Blot
Concentration:
1.5 mg/mL
Formulation:
PBS with 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
A8MXV4
Gene Symbols:
NUDT19
Immunogen:
Synthetic peptide of human NUDT19
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG