PIMA534640
DKC1 Recombinant Rabbit Monoclonal Antibody (JU34-32), Invitrogen™
Manufacturer: Thermo Scientific
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | PIMA534640-Each-of-1 | In Stock | ₹ 45,646.26 |
PIMA534640 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 45,646.26
GST (18%): ₹ 8,216.327
Total Price: ₹ 53,862.587
Antigen
DKC1
Classification
Monoclonal
Concentration
1 mg/mL
Formulation
TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.
O60832
Gene Symbols
DKC1
Immunogen
Synthetic peptide within Human DKC1 aa 353-402
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human
Product Type
Antibody
Isotype
IgG
Applications
Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Clone
JU34-32
Conjugate
Unconjugated
Gene
DKC1
Gene Alias
BC068171; CBF5; CBF5 homolog; DKC; DKC1; DKCX; dyskeratosis congenita 1, dyskerin; dyskeratosis congenita 1, dyskerin homolog; dyskerin; dyskerin pseudouridine synthase 1; H/ACA ribonucleoprotein complex subunit 4; H/ACA ribonucleoprotein complex subunit DKC1; Nap57; NOLA4; Nopp140-associated protein of 57 kDa; nucleolar protein family A member 4; Nucleolar protein NAP57; snoRNP protein DKC1; XAP101
Host Species
Rabbit
Purification Method
Protein A
Regulatory Status
RUO
Gene ID (Entrez)
1736
Content And Storage
-20° C, Avoid Freeze/Thaw Cycles, store in dark
Form
Liquid
Related Products
Description
- Positive Control: A431, rat brain tissue, human kidney tissue, mouse testis tissue
- This gene is a member of the H/ACA snoRNPs gene family
- snoRNPs are involved in various aspects of rRNA processing and modification and have been classified into two families: C/D and H/ACA
- The H/ACA snoRNPs also include the NOLA1, 2 and 3 proteins
- The protein encoded by this gene and the three NOLA proteins localize to the dense fibrillar components of nucleoli and to coiled bodies in the nucleus
- Both 18S rRNA production and rRNA pseudouridylation are impaired if any one of the four proteins is depleted
- These four H/ACA snoRNP proteins are also components of the telomerase complex
- The protein encoded by this gene is related to the Saccharomyces cerevisiae Cbf5p and Drosophila melanogaster Nop60B proteins
- The gene lies in a tail-to-tail orientation with the palmitoylated erythrocyte membrane protein gene and is transcribed in a telomere to centromere direction
- Both nucleotide substitutions and single trinucleotide repeat polymorphisms have been found in this gene
- Mutations in this gene cause X-linked dyskeratosis congenita, a disease resulting in reticulate skin pigmentation, mucosal leukoplakia, nail dystrophy, and progressive bone marrow failure in most cases
- Mutations in this gene also cause Hoyeraal-Hreidarsson syndrome, which is a more severe form of dyskeratosis congenita
- Two transcript variants encoding different isoforms have been found for this gene.
Compare Similar Items
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Antigen: DKC1
Classification: Monoclonal
Concentration: 1 mg/mL
Formulation: TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: O60832
Gene Symbols: DKC1
Immunogen: Synthetic peptide within Human DKC1 aa 353-402
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Applications: Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Clone: JU34-32
Conjugate: Unconjugated
Gene: DKC1
Gene Alias: BC068171; CBF5; CBF5 homolog; DKC; DKC1; DKCX; dyskeratosis congenita 1, dyskerin; dyskeratosis congenita 1, dyskerin homolog; dyskerin; dyskerin pseudouridine synthase 1; H/ACA ribonucleoprotein complex subunit 4; H/ACA ribonucleoprotein complex subunit DKC1; Nap57; NOLA4; Nopp140-associated protein of 57 kDa; nucleolar protein family A member 4; Nucleolar protein NAP57; snoRNP protein DKC1; XAP101
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 1736
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles, store in dark
Form: Liquid
Antigen:
DKC1
Classification:
Monoclonal
Concentration:
1 mg/mL
Formulation:
TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
O60832
Gene Symbols:
DKC1
Immunogen:
Synthetic peptide within Human DKC1 aa 353-402
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Applications:
Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Clone:
JU34-32
Conjugate:
Unconjugated
Gene:
DKC1
Gene Alias:
BC068171; CBF5; CBF5 homolog; DKC; DKC1; DKCX; dyskeratosis congenita 1, dyskerin; dyskeratosis congenita 1, dyskerin homolog; dyskerin; dyskerin pseudouridine synthase 1; H/ACA ribonucleoprotein complex subunit 4; H/ACA ribonucleoprotein complex subunit DKC1; Nap57; NOLA4; Nopp140-associated protein of 57 kDa; nucleolar protein family A member 4; Nucleolar protein NAP57; snoRNP protein DKC1; XAP101
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
1736
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles, store in dark
Form:
Liquid
Antigen: MATR3
Classification: Monoclonal
Concentration: 1 mg/mL
Formulation: TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: P43243
Gene Symbols: MATR3
Immunogen: Synthetic peptide within Human Matrin 3 aa 749-798
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Applications: Flow Cytometry, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Clone: JU93-43
Conjugate: Unconjugated
Gene: MATR3
Gene Alias: 1110061A14Rik; 2810017I02Rik; AI841759; ALS21; AW555618; D030046F20Rik; KIAA0723; MATR3; matrin 3; matrin-3; matrin-3-like protein; mKIAA0723; MPD2; nuclear scaffold protein P130/MAT3; P130/MAT3; VCPDM; vocal cord and pharyngeal weakness with distal myopathy
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 9782
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles, store in dark
Form: Liquid
Antigen:
MATR3
Classification:
Monoclonal
Concentration:
1 mg/mL
Formulation:
TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
P43243
Gene Symbols:
MATR3
Immunogen:
Synthetic peptide within Human Matrin 3 aa 749-798
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Applications:
Flow Cytometry, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Clone:
JU93-43
Conjugate:
Unconjugated
Gene:
MATR3
Gene Alias:
1110061A14Rik; 2810017I02Rik; AI841759; ALS21; AW555618; D030046F20Rik; KIAA0723; MATR3; matrin 3; matrin-3; matrin-3-like protein; mKIAA0723; MPD2; nuclear scaffold protein P130/MAT3; P130/MAT3; VCPDM; vocal cord and pharyngeal weakness with distal myopathy
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
9782
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles, store in dark
Form:
Liquid
Antigen: ILF2
Classification: Monoclonal
Concentration: 1 mg/mL
Formulation: TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: Q12905
Gene Symbols: ILF2
Immunogen: Synthetic peptide within Human ILF2 aa 245-294
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Applications: Flow Cytometry, Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot
Clone: JU50-33
Conjugate: Unconjugated
Gene: ILF2
Gene Alias: 6230405A16Rik; Ab1-143; ILF2; interleukin enhancer binding factor 2; interleukin enhancer binding factor 2, 45kD; interleukin enhancer binding factor 2, 45kDa; interleukin enhancer-binding factor 2; Interleukin enhancer-binding factor 2 homolog; liver regeneration-related protein LRRG031; MGC8391; Nf45; nuclear factor of activated T-cells 45 kDa; nuclear factor of activated T-cells, 45-kDa; PRO3063; TEG-267; testis expressed gene 267; Tex261; Tex267; Unknown (protein for MGC:134524); wu:fb34h01; zgc:73084; zgc:77276
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 3608
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles, store in dark
Form: Liquid
Antigen:
ILF2
Classification:
Monoclonal
Concentration:
1 mg/mL
Formulation:
TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
Q12905
Gene Symbols:
ILF2
Immunogen:
Synthetic peptide within Human ILF2 aa 245-294
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Applications:
Flow Cytometry, Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot
Clone:
JU50-33
Conjugate:
Unconjugated
Gene:
ILF2
Gene Alias:
6230405A16Rik; Ab1-143; ILF2; interleukin enhancer binding factor 2; interleukin enhancer binding factor 2, 45kD; interleukin enhancer binding factor 2, 45kDa; interleukin enhancer-binding factor 2; Interleukin enhancer-binding factor 2 homolog; liver regeneration-related protein LRRG031; MGC8391; Nf45; nuclear factor of activated T-cells 45 kDa; nuclear factor of activated T-cells, 45-kDa; PRO3063; TEG-267; testis expressed gene 267; Tex261; Tex267; Unknown (protein for MGC:134524); wu:fb34h01; zgc:73084; zgc:77276
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
3608
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles, store in dark
Form:
Liquid
Antigen: PFKM
Classification: Monoclonal
Concentration: 1 mg/mL
Formulation: TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.: P08237
Gene Symbols: PFKM
Immunogen: Synthetic peptide within Human Fructose 6 Phosphate Kinase aa 107-156
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Applications: Flow Cytometry, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Clone: JU53-31
Conjugate: Unconjugated
Gene: PFKM
Gene Alias: 6-phosphofructo-1-kinase; 6-phosphofructokinase type A; 6-phosphofructokinase, muscle type; AI131669; ATP-dependent 6-phosphofructokinase, muscle type; ATP-dependent 6-phosphofructokinase, muscle type {ECO:0000255; ATP-PFK; ATP-PFK {ECO:0000255; GSD7; HAMAP-Rule:MF_03184}; PFK; PFK1; PFK-1; Pfk4; Pfk-4; Pfka; PFK-A; PFKM; Pfk-m; PFKX; Phosphofructo-1-kinase isozyme A; phosphofructokinase 1; phosphofructokinase 4; phosphofructokinase M variant 3/4; phosphofructokinase muscle; phosphofructokinase, muscle; phosphofructokinase, polypeptide X; phosphofructokinase-1 A isozyme; phosphofructokinase-A; phosphofructokinase-M; phosphofructokinase-M (connecting peptide); phosphohexokinase; phosphohexokinase {ECO:0000255; PPP1R122; protein phosphatase 1, regulatory subunit 122
Host Species: Rabbit
Purification Method: Protein A
Regulatory Status: RUO
Gene ID (Entrez): 5213
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles, store in dark
Form: Liquid
Antigen:
PFKM
Classification:
Monoclonal
Concentration:
1 mg/mL
Formulation:
TBS with 0.05% BSA, 40% glycerol and 0.05% sodium azide; pH 7.4
Gene Accession No.:
P08237
Gene Symbols:
PFKM
Immunogen:
Synthetic peptide within Human Fructose 6 Phosphate Kinase aa 107-156
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Applications:
Flow Cytometry, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Clone:
JU53-31
Conjugate:
Unconjugated
Gene:
PFKM
Gene Alias:
6-phosphofructo-1-kinase; 6-phosphofructokinase type A; 6-phosphofructokinase, muscle type; AI131669; ATP-dependent 6-phosphofructokinase, muscle type; ATP-dependent 6-phosphofructokinase, muscle type {ECO:0000255; ATP-PFK; ATP-PFK {ECO:0000255; GSD7; HAMAP-Rule:MF_03184}; PFK; PFK1; PFK-1; Pfk4; Pfk-4; Pfka; PFK-A; PFKM; Pfk-m; PFKX; Phosphofructo-1-kinase isozyme A; phosphofructokinase 1; phosphofructokinase 4; phosphofructokinase M variant 3/4; phosphofructokinase muscle; phosphofructokinase, muscle; phosphofructokinase, polypeptide X; phosphofructokinase-1 A isozyme; phosphofructokinase-A; phosphofructokinase-M; phosphofructokinase-M (connecting peptide); phosphohexokinase; phosphohexokinase {ECO:0000255; PPP1R122; protein phosphatase 1, regulatory subunit 122
Host Species:
Rabbit
Purification Method:
Protein A
Regulatory Status:
RUO
Gene ID (Entrez):
5213
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles, store in dark
Form:
Liquid