PIPA539382

CHML Polyclonal Antibody, Invitrogen™

Manufacturer: Thermo Scientific

Select a Size

Pack Size SKU Availability Price
Each of 1 PIPA539382-Each-of-1 In Stock ₹ 42,694.44

PIPA539382 - Each of 1

₹ 42,694.44

In Stock

Quantity

1

Base Price: ₹ 42,694.44

GST (18%): ₹ 7,684.999

Total Price: ₹ 50,379.439

Antigen

CHML

Classification

Polyclonal

Conjugate

Unconjugated

Gene

CHML

Gene Alias

Rab proteins geranylgeranyltransferase component A 2, Choroideremia-like protein, Rab escort protein 2, REP-2, REP2

Host Species

Rabbit

Purification Method

Antigen affinity chromatography

Regulatory Status

RUO

Gene ID (Entrez)

1122

Content And Storage

-20°C

Form

Liquid

Applications

Immunohistochemistry (Paraffin), Western Blot

Concentration

1 mg/mL

Formulation

Dulbecco′s PBS with 150mM NaCl, 50% glycerol and 0.02% sodium azide; pH 7.4

Gene Accession No.

P26374

Gene Symbols

CHML

Immunogen

A synthetic peptide derived from the internal region of human CHML

Quantity

100 μg

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Isotype

IgG

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Description

  • Two isoforms of the REP gene have been isolated, REP-1 and REP-2
  • The REP-1 gene, located on chromosome Xq21, is prone to a wide variety of mutations, including nonsense, frameshift and splice-site mutations and deletions
  • In patients with choroideraemia (CHM), mutations in the REP-1 gene result in progressive dystrophy of the choroid, retinal pigment epithelium and retina
  • CHM is an X-linked hereditary eye disease that leads to blindness later in life
  • REP-2 is able to bind to several Rab proteins with the same affinity as REP-1 and may act a substitute for REP-1 to prevent widespread tissue abnormalities in patients with CHM.

Compare Similar Items

Show Difference

Img

Thermo Scientific

PIPA539382

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Antigen:
CHML

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
CHML

Gene Alias:
Rab proteins geranylgeranyltransferase component A 2, Choroideremia-like protein, Rab escort protein 2, REP-2, REP2

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
1122

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 mg/mL

Formulation:
Dulbecco′s PBS with 150mM NaCl, 50% glycerol and 0.02% sodium azide; pH 7.4

Gene Accession No.:
P26374

Gene Symbols:
CHML

Immunogen:
A synthetic peptide derived from the internal region of human CHML

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA539384

--


Antigen:
RAB11FIP4

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
RAB11FIP4

Gene Alias:
RAB11-FIP4, RAB11 family interacting protein 4 class II

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
268451, 84440

Content And Storage:
-20°C

Form:
Liquid

Applications:
Western Blot

Concentration:
1 mg/mL

Formulation:
Dulbecco′s PBS with 150mM NaCl, 50% glycerol and 0.02% sodium azide; pH 7.4

Gene Accession No.:
Q86YS3, Q8BQP8

Gene Symbols:
RAB11FIP4

Immunogen:
A synthetic peptide derived from the internal region of human RAB11FIP4

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human, Mouse

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA539385

--


Antigen:
RAB3GAP1

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
RAB3GAP1

Gene Alias:
Rab3 GTPase-activating protein catalytic subunit, RAB3 GTPase-activating protein 130 kDa subunit, Rab3-GAP p130, Rab3-GAP, KIAA0066, RAB3GAP, Rab 3 GAP p130, Rab3 GAP p130

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
22930

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 mg/mL

Formulation:
Dulbecco′s PBS with 150mM NaCl, 50% glycerol and 0.02% sodium azide; pH 7.4

Gene Accession No.:
Q15042

Gene Symbols:
RAB3GAP1

Immunogen:
A synthetic peptide derived from the internal region of human RAB3GAP1

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

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PIPA539386

--


Antigen:
RAB3GAP2

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
RAB3GAP2

Gene Alias:
RAB3-GAP150, RAB3GAP150, WARBM2, p150, RGAP-iso, rab3 GTPase-activating protein 150 kDa subunit, rab3 GTPase-activating protein non-catalytic subunit, rab3-GAP p150, rab3-GAP regulatory subunit

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
25782, 289350, 98732

Content And Storage:
-20°C

Form:
Liquid

Applications:
Immunohistochemistry (Paraffin), Western Blot

Concentration:
1 mg/mL

Formulation:
Dulbecco′s PBS with 150mM NaCl, 50% glycerol and 0.02% sodium azide; pH 7.4

Gene Accession No.:
Q9H2M9, Q8BMG7, Q5U1Z0

Gene Symbols:
RAB3GAP2

Immunogen:
A synthetic peptide derived from the internal region of human RAB3GAP2

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human, Mouse, Non-human Primate, Rat

Product Type:
Antibody

Isotype:
IgG