PIPA553546

Dysferlin Polyclonal Antibody, Invitrogen™

Manufacturer: Thermo Scientific

Select a Size

Pack Size SKU Availability Price
Each of 1 PIPA553546-Each-of-1 In Stock ₹ 49,710.36

PIPA553546 - Each of 1

₹ 49,710.36

In Stock

Quantity

1

Base Price: ₹ 49,710.36

GST (18%): ₹ 8,947.865

Total Price: ₹ 58,658.225

Antigen

Dysferlin

Classification

Polyclonal

Conjugate

Unconjugated

Gene

DYSF

Gene Alias

2310004N10Rik; AI604795; D6Pas3; Dysf; Dysferlin; dysferlin variant a; dysferlin_a; dystrophy-associated fer-1-like 1; dystrophy-associated fer-1-like protein; FER1L1; fer-1-like family member 1; fer-1-like protein 1; FLJ00175; FLJ90168; LGMD2B; limb girdle muscular dystrophy 2B (autosomal recessive); MMD1

Host Species

Rabbit

Purification Method

Antigen affinity chromatography

Regulatory Status

RUO

Gene ID (Entrez)

8291

Content And Storage

Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form

Liquid

Applications

Immunocytochemistry, Immunohistochemistry

Concentration

0.2 mg/mL

Formulation

PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.

O75923

Gene Symbols

DYSF

Immunogen

Recombinant protein corresponding to Human Dysferlin

Quantity

100 μL

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Isotype

IgG

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Description

  • Immunogen sequence: IVVELYDHDT YGADEFMGRC ICQPSLERMP RLAWFPLTRG SQPSGELLAS FELIQREKPA IHHIPGFEVQ ETSRILDESE DTDLPYPPPQ REANIYMVPQ NIKPALQRTA IEILAWG Highest antigen sequence identity to the following orthologs: Mouse - 96%, Rat - 96%
  • Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM)
  • Dysferlin is normally localized to the muscle plasma membrane
  • In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation
  • This antibody is used for the characterization of LGMD2B and MM.

Compare Similar Items

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Img

Thermo Scientific

PIPA553546

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Antigen:
Dysferlin

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
DYSF

Gene Alias:
2310004N10Rik; AI604795; D6Pas3; Dysf; Dysferlin; dysferlin variant a; dysferlin_a; dystrophy-associated fer-1-like 1; dystrophy-associated fer-1-like protein; FER1L1; fer-1-like family member 1; fer-1-like protein 1; FLJ00175; FLJ90168; LGMD2B; limb girdle muscular dystrophy 2B (autosomal recessive); MMD1

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
8291

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunocytochemistry, Immunohistochemistry

Concentration:
0.2 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
O75923

Gene Symbols:
DYSF

Immunogen:
Recombinant protein corresponding to Human Dysferlin

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA553547

--


Antigen:
PTGFRN

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
PTGFRN

Gene Alias:
4833445A08Rik; AU042434; CD315; CD9 partner 1; CD9P1; CD9P-1; EWIF; EWI-F; FPRP; Glu-Trp-Ile EWI motif-containing protein F; KIAA1436; prostaglandin F2 receptor inhibitor; prostaglandin F2 receptor negative regulator; Prostaglandin F2-alpha receptor regulatory protein; prostaglandin F2-alpha receptor-associated protein; Ptgfrn; SMAP-6; Trim45

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
5738

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunohistochemistry

Concentration:
0.1 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
Q9P2B2

Gene Symbols:
PTGFRN

Immunogen:
Recombinant protein corresponding to Human PTGFRN

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA553548

--


Antigen:
GALNT15

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
GALNT15

Gene Alias:
4631401E18Rik; GALNACT15; GalNAc-T-like protein 2; GALNT13; GALNT15; GALNT7; Galntl2; mpp-GalNAc-T15; PIH5; polypeptide GalNAc transferase 15; polypeptide GalNAc transferase-like protein 2; polypeptide N-acetylgalactosaminyltransferase 13; polypeptide N-acetylgalactosaminyltransferase 15; polypeptide N-acetylgalactosaminyltransferase-like 2; polypeptide N-acetylgalactosaminyltransferase-like protein 2; pp-GalNAc-T15; pp-GaNTase-like protein 2; pregnancy-induced hypertension syndrome-related protein 5; protein-UDP acetylgalactosaminyltransferase-like protein 2; UDP-GalNAc transferase T15; UDP-GalNAc:polypeptide N-acetylgalactosaminyltransferase-like protein 2; UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 15; UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 7; UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase-like 2; UNQ770/PRO1564

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
117248

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunocytochemistry, Immunohistochemistry

Concentration:
0.2 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
Q8N3T1

Gene Symbols:
GALNT15

Immunogen:
Recombinant protein corresponding to Human GALNT15

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA553549

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Antigen:
SQRDL

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
Sqor

Gene Alias:
0610039J17Rik; 4930557M22Rik; Cc2-17; CGI-44; flavo-binding protein; PRO1975; SQOR; Sqrdl; sulfide dehydrogenase like; Sulfide dehydrogenase-like; Sulfide quinone oxidoreductase; sulfide quinone reductase-like (yeast); sulfide:quinone oxidoreductase, mitochondrial

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
58472, 59010

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunocytochemistry, Immunohistochemistry, Western Blot

Concentration:
0.25 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
Q9R112, Q9Y6N5

Gene Symbols:
Sqor

Immunogen:
Recombinant protein corresponding to Human SQRDL

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human, Mouse

Product Type:
Antibody

Isotype:
IgG