PIPA564260

CLN6 Polyclonal Antibody, Invitrogen™

Manufacturer: Thermo Scientific

Select a Size

Pack Size SKU Availability Price
Each of 1 PIPA564260-Each-of-1 In Stock ₹ 47,015.22

PIPA564260 - Each of 1

₹ 47,015.22

In Stock

Quantity

1

Base Price: ₹ 47,015.22

GST (18%): ₹ 8,462.74

Total Price: ₹ 55,477.96

Antigen

CLN6

Classification

Polyclonal

Conjugate

Unconjugated

Gene

CLN6

Gene Alias

1810065L06Rik; AW743417; ceroid-lipofuscinosis; ceroid-lipofuscinosis neuronal 6 late infantile; ceroid-lipofuscinosis neuronal protein 6; ceroid-lipofuscinosis, neuronal 6; ceroid-lipofuscinosis, neuronal 6, late infantile, variant; CLN4A; CLN6; D9Bwg1455e; HsT18960; nclf; neuronal ceroid lipofuscinosis; Protein CLN6

Host Species

Rabbit

Purification Method

Antigen affinity chromatography

Regulatory Status

RUO

Gene ID (Entrez)

54982

Content And Storage

Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form

Liquid

Applications

Immunohistochemistry, Western Blot

Concentration

0.05 mg/mL

Formulation

PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.

Q9NWW5

Gene Symbols

CLN6

Immunogen

Recombinant protein corresponding to Human CLN6

Quantity

100 μL

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Isotype

IgG

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Description

  • Immunogen sequence: WNDPVLRKKY PGVIYVPEPW AFYTLHVSSR Highest antigen sequence identity to the following orthologs: Mouse - 97%, Rat - 93%
  • CLN6, a 311-amino acid protein, has 7 predicted transmembrane domains and is conserved across vertebrates
  • The CLN6 protein localizes to the endoplasmic reticulum but contributes to lysosomal function
  • Mutations in the CLN6 gene cause variant late-onset infantile neuronal ceroid lipofuscinosis (vLINCL), a lysosomal storage disorder marked by progressive mental deterioration and blindness; part of a group of severe inherited neurodegenerative disorders affecting children wherein lysosomes accumulate storage material, causing the death of neurons
  • CLN6 is one of eight proteins, including CLN1-8, that are associated with NCL.

Compare Similar Items

Show Difference

Img

Thermo Scientific

PIPA564260

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Antigen:
CLN6

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
CLN6

Gene Alias:
1810065L06Rik; AW743417; ceroid-lipofuscinosis; ceroid-lipofuscinosis neuronal 6 late infantile; ceroid-lipofuscinosis neuronal protein 6; ceroid-lipofuscinosis, neuronal 6; ceroid-lipofuscinosis, neuronal 6, late infantile, variant; CLN4A; CLN6; D9Bwg1455e; HsT18960; nclf; neuronal ceroid lipofuscinosis; Protein CLN6

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
54982

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunohistochemistry, Western Blot

Concentration:
0.05 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
Q9NWW5

Gene Symbols:
CLN6

Immunogen:
Recombinant protein corresponding to Human CLN6

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

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PIPA564263

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Antigen:
C9orf69

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
TMEM250

Gene Alias:
C9orf69; chromosome 9 open reading frame 69; herpes virus UL25-binding protein; protein C9orf69; TMEM250; Transmembrane protein 250

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
90120

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunocytochemistry, Immunohistochemistry

Concentration:
0.1 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
H0YL14

Gene Symbols:
TMEM250

Immunogen:
Recombinant protein corresponding to Human C9orf69

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

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PIPA564264

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Antigen:
NUDT6

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
NUDT6

Gene Alias:
antisense basic fibroblast growth factor; Antisense basic fibroblast growth factor B; anti-sense basic fibroblast growth factor B; ASFGF2; Asfgf2b; FGF2AS; FGF-AS; Gfg; GFG1; GFG-1; Nucleoside diphosphate-linked moiety X motif 6; nudix (nucleoside diphosphate linked moiety X)-type motif 6; nudix hydrolase 6; nudix motif 6; Nudt6; Protein GFG

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
11162

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunohistochemistry

Concentration:
0.1 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
P53370

Gene Symbols:
NUDT6

Immunogen:
Recombinant protein corresponding to Human NUDT6

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

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PIPA564265

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Antigen:
PIBF1

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
PIBF1

Gene Alias:
C13orf24; Centrosomal protein of 90 kDa; CEP90; PIBF; PIBF1; progesterone immunomodulatory binding factor 1; progesterone-induced blocking factor 1; progesterone-induced-blocking factor 1; RGD1305077; RP11-505F3.1

Host Species:
Rabbit

Purification Method:
Antigen affinity chromatography

Regulatory Status:
RUO

Gene ID (Entrez):
10464

Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.

Form:
Liquid

Applications:
Immunohistochemistry

Concentration:
0.1 mg/mL

Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2

Gene Accession No.:
Q8WXW3

Gene Symbols:
PIBF1

Immunogen:
Recombinant protein corresponding to Human PIBF1

Quantity:
100 μL

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG