PIPA564937
GCS1 Polyclonal Antibody, Invitrogen™
Manufacturer: Thermo Scientific
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | PIPA564937-Each-of-1 | In Stock | ₹ 47,015.22 |
PIPA564937 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 47,015.22
GST (18%): ₹ 8,462.74
Total Price: ₹ 55,477.96
Antigen
GCS1
Classification
Polyclonal
Conjugate
Unconjugated
Gene
MOGS
Gene Alias
1810017N02Rik; AI181835; CDG2B; CWH41; DER7; GCS1; Glucosidase 1; glucosidase I; glycoprotein-processing glucosidase I; Mannosyl-oligosaccharide glucosidase; Mogs; Processing A-glucosidase I
Host Species
Rabbit
Purification Method
Antigen affinity chromatography
Regulatory Status
RUO
Gene ID (Entrez)
7841
Content And Storage
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form
Liquid
Applications
Immunocytochemistry, Western Blot
Concentration
0.05 mg/mL
Formulation
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.
Q13724
Gene Symbols
MOGS
Immunogen
Recombinant Human GCS1
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human
Product Type
Antibody
Isotype
IgG
Related Products
Description
- Immunogen sequence: LESHAEGFRER FEKTFQLKEK GLSSGEQVLG QAALSGLLGG IGYFYGQGLV LPDIGVEGSE QKVDPALFPP VPLFTAVPSR SFFPRGFLWD EGFHQLVVQR WDPSLTREAL GHWLGLLNAD GWIG Highest antigen sequence identity to the following orthologs - mouse 89%, rat 88%
- GCS1 cleaves the distal alpha 1,2-linked glucose residue from the Glc(3)Man(9)GlcNAc(2) oligosaccharide precursor in a highly specific manner
- Defects in GCS1 are the cause of type IIb congenital disorder of glycosylation (CDGIIb)
- This syndrome is also known as glucosidase I deficiency and is characterized by marked generalized hypotonia and hypomotility of the neonate, dysmorphic features, including a prominent occiput, short palpebral fissures, retrognathia, high arched palate, generalized edema, and hypoplastic genitalia
- Symptoms include hepatomegaly, hypoventilation, feeding problems and seizures
- The clinical course is progressive and survival is at most a few months.
Compare Similar Items
Show Difference
Antigen: GCS1
Classification: Polyclonal
Conjugate: Unconjugated
Gene: MOGS
Gene Alias: 1810017N02Rik; AI181835; CDG2B; CWH41; DER7; GCS1; Glucosidase 1; glucosidase I; glycoprotein-processing glucosidase I; Mannosyl-oligosaccharide glucosidase; Mogs; Processing A-glucosidase I
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 7841
Content And Storage: Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form: Liquid
Applications: Immunocytochemistry, Western Blot
Concentration: 0.05 mg/mL
Formulation: PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.: Q13724
Gene Symbols: MOGS
Immunogen: Recombinant Human GCS1
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
GCS1
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
MOGS
Gene Alias:
1810017N02Rik; AI181835; CDG2B; CWH41; DER7; GCS1; Glucosidase 1; glucosidase I; glycoprotein-processing glucosidase I; Mannosyl-oligosaccharide glucosidase; Mogs; Processing A-glucosidase I
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
7841
Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form:
Liquid
Applications:
Immunocytochemistry, Western Blot
Concentration:
0.05 mg/mL
Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.:
Q13724
Gene Symbols:
MOGS
Immunogen:
Recombinant Human GCS1
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: FAM134A
Classification: Polyclonal
Conjugate: Unconjugated
Gene: RETREG2
Gene Alias: C2H2orf17; C2orf17; Fam134a; family with sequence similarity 134 member A; family with sequence similarity 134, member A; MAG2; MAG-2; metastasis associated gene-2; protein FAM134A; reticulophagy regulator 2; reticulophagy regulator 2; protein FAM134A; reticulophagy regulator family member 2; Retreg2; RGD1306844; zgc:158472
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 79137
Content And Storage: Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form: Liquid
Applications: Immunocytochemistry
Concentration: 0.1 mg/mL
Formulation: PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.: Q8NC44
Gene Symbols: RETREG2
Immunogen: Recombinant Human FAM134A
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
FAM134A
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
RETREG2
Gene Alias:
C2H2orf17; C2orf17; Fam134a; family with sequence similarity 134 member A; family with sequence similarity 134, member A; MAG2; MAG-2; metastasis associated gene-2; protein FAM134A; reticulophagy regulator 2; reticulophagy regulator 2; protein FAM134A; reticulophagy regulator family member 2; Retreg2; RGD1306844; zgc:158472
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
79137
Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form:
Liquid
Applications:
Immunocytochemistry
Concentration:
0.1 mg/mL
Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.:
Q8NC44
Gene Symbols:
RETREG2
Immunogen:
Recombinant Human FAM134A
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: KCT2
Classification: Polyclonal
Conjugate: Unconjugated
Gene: C5orf15
Gene Alias: 9530068E07Rik; C5orf15; C85061; chromosome 5 open reading frame 15; HTGN29; Kct2; keratinocyte-associated transmembrane protein 2; keratinocytes associated transmembrane protein 2; RIKEN cDNA 9530068E07 gene
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 56951
Content And Storage: Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form: Liquid
Applications: Immunocytochemistry
Concentration: 0.1 mg/mL
Formulation: PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.: Q8NC54
Gene Symbols: C5orf15
Immunogen: Recombinant Human KCT2
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
KCT2
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
C5orf15
Gene Alias:
9530068E07Rik; C5orf15; C85061; chromosome 5 open reading frame 15; HTGN29; Kct2; keratinocyte-associated transmembrane protein 2; keratinocytes associated transmembrane protein 2; RIKEN cDNA 9530068E07 gene
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
56951
Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form:
Liquid
Applications:
Immunocytochemistry
Concentration:
0.1 mg/mL
Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.:
Q8NC54
Gene Symbols:
C5orf15
Immunogen:
Recombinant Human KCT2
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG
Antigen: FAM134B
Classification: Polyclonal
Conjugate: Unconjugated
Gene: RETREG1
Gene Alias: 1810015C04Rik; AU015349; FAM134B; family with sequence similarity 134 member B; family with sequence similarity 134, member B; hypothetical protein FLJ20152; hypothetical protein LOC540068; JK1; JK-1; protein FAM134B; Protein FAM134B-like protein; reticulophagy receptor 1; reticulophagy receptor FAM134B; reticulophagy regulator 1; Retreg1
Host Species: Rabbit
Purification Method: Antigen affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 54463
Content And Storage: Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form: Liquid
Applications: Immunocytochemistry
Concentration: 0.2 mg/mL
Formulation: PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.: Q9H6L5
Gene Symbols: RETREG1
Immunogen: Recombinant Human FAM134B
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Product Type: Antibody
Isotype: IgG
Antigen:
FAM134B
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
RETREG1
Gene Alias:
1810015C04Rik; AU015349; FAM134B; family with sequence similarity 134 member B; family with sequence similarity 134, member B; hypothetical protein FLJ20152; hypothetical protein LOC540068; JK1; JK-1; protein FAM134B; Protein FAM134B-like protein; reticulophagy receptor 1; reticulophagy receptor FAM134B; reticulophagy regulator 1; Retreg1
Host Species:
Rabbit
Purification Method:
Antigen affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
54463
Content And Storage:
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form:
Liquid
Applications:
Immunocytochemistry
Concentration:
0.2 mg/mL
Formulation:
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Gene Accession No.:
Q9H6L5
Gene Symbols:
RETREG1
Immunogen:
Recombinant Human FAM134B
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Product Type:
Antibody
Isotype:
IgG