PIPA588726
GCS1 Polyclonal Antibody, Invitrogen™
Manufacturer: Thermo Scientific
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | PIPA588726-Each-of-1 | In Stock | ₹ 44,705.10 |
PIPA588726 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 44,705.10
GST (18%): ₹ 8,046.918
Total Price: ₹ 52,752.018
Antigen
GCS1
Classification
Polyclonal
Conjugate
Unconjugated
Gene
MOGS
Gene Alias
1810017N02Rik, AI181835, CDG2B, CWH41, DER7, GCS1, Glucosidase 1, glucosidase I, glycoprotein-processing glucosidase I, Mannosyl-oligosaccharide glucosidase, Mogs, Processing A-glucosidase I
Host Species
Rabbit
Purification Method
Affinity Chromatography
Regulatory Status
RUO
Gene ID (Entrez)
57377, 7841
Content And Storage
-20° C, Avoid Freeze/Thaw Cycles
Form
Liquid
Applications
Western Blot
Concentration
0.70 mg/mL
Formulation
PBS with 50% glycerol and 0.01% thimerosal, pH 7.3
Gene Accession No.
Q13724, Q80UM7
Gene Symbols
MOGS
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 60-320 of human MOGS (NP_0062932)
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human, Mouse, Rat
Product Type
Antibody
Isotype
IgG
Related Products
Description
- Immunogen sequence: RWVLAWYRAR RAVTLHSAPP VLPADSSSPA VAPDLFWGTY RPHVYFGMKT RSPKPLLTGL MWAQQGTTPG TPKLRHTCEQ GDGVGPYGWE FHDGLSFGRQ HIQDGALRLT TEFVKRPGGQ HGGDWSWRVT VEPQDSGTSA LPLVSLFFYV VTDGKEVLLP EVGAKGQLKF ISGHTSELGD FRFTLLPPTS PGDTAPKYGS YNVFWTSNPG LPLLTEMVKS RLNSWFQHRP PGAPPERYLG LPGSLKWEDR GPSGQGQGQF L; Positive Samples: U-87MG, LO2, BxPC-3, OVCAR-3, Mouse Brain, Mouse Liver, Mouse Pancreas, Mouse Testis, Rat Liver; Cellular Location: Endoplasmic reticulum membrane, Single-pass type II membrane protein GCS1 cleaves the distal alpha 1,2-linked glucose residue from the Glc(3)Man(9)GlcNAc(2) oligosaccharide precursor in a highly specific manner
- Defects in GCS1 are the cause of type IIb congenital disorder of glycosylation (CDGIIb)
- This syndrome is also known as glucosidase I deficiency and is characterized by marked generalized hypotonia and hypomotility of the neonate, dysmorphic features, including a prominent occiput, short palpebral fissures, retrognathia, high arched palate, generalized edema, and hypoplastic genitalia
- Symptoms include hepatomegaly, hypoventilation, feeding problems and seizures
- The clinical course is progressive and survival is at most a few months.
Compare Similar Items
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Antigen: GCS1
Classification: Polyclonal
Conjugate: Unconjugated
Gene: MOGS
Gene Alias: 1810017N02Rik, AI181835, CDG2B, CWH41, DER7, GCS1, Glucosidase 1, glucosidase I, glycoprotein-processing glucosidase I, Mannosyl-oligosaccharide glucosidase, Mogs, Processing A-glucosidase I
Host Species: Rabbit
Purification Method: Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 57377, 7841
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles
Form: Liquid
Applications: Western Blot
Concentration: 0.70 mg/mL
Formulation: PBS with 50% glycerol and 0.01% thimerosal, pH 7.3
Gene Accession No.: Q13724, Q80UM7
Gene Symbols: MOGS
Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 60-320 of human MOGS (NP_0062932)
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
GCS1
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
MOGS
Gene Alias:
1810017N02Rik, AI181835, CDG2B, CWH41, DER7, GCS1, Glucosidase 1, glucosidase I, glycoprotein-processing glucosidase I, Mannosyl-oligosaccharide glucosidase, Mogs, Processing A-glucosidase I
Host Species:
Rabbit
Purification Method:
Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
57377, 7841
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles
Form:
Liquid
Applications:
Western Blot
Concentration:
0.70 mg/mL
Formulation:
PBS with 50% glycerol and 0.01% thimerosal, pH 7.3
Gene Accession No.:
Q13724, Q80UM7
Gene Symbols:
MOGS
Immunogen:
Recombinant fusion protein containing a sequence corresponding to amino acids 60-320 of human MOGS (NP_0062932)
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG
Antigen: UQCRB
Classification: Polyclonal
Conjugate: Unconjugated
Gene: UQCRB
Gene Alias: 2210415M14Rik, Complex III subunit 7, complex III subunit VII, Cytochrome b-c1 complex subunit 7, MC3DN3, mitochondrial ubiquinone-binding protein, QCR7, QPC, QP-C, ubiquinol-cytochrome c reductase binding protein, ubiquinol-cytochrome c reductase binding protein-like, ubiquinol-cytochrome c reductase complex 14 kDa protein, ubiquinol-cytochrome c reductase, complex III subunit VI, UQBC, UQBP, UQCR6, Uqcrb, Uqcrbl, UQPC
Host Species: Rabbit
Purification Method: Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 362897, 67530, 7381
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles
Form: Liquid
Applications: Western Blot
Concentration: 2.15 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide, pH 7.3
Gene Accession No.: P14927, Q9D855
Gene Symbols: UQCRB
Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 1-111 of human UQCRB (NP_0062851)
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
UQCRB
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
UQCRB
Gene Alias:
2210415M14Rik, Complex III subunit 7, complex III subunit VII, Cytochrome b-c1 complex subunit 7, MC3DN3, mitochondrial ubiquinone-binding protein, QCR7, QPC, QP-C, ubiquinol-cytochrome c reductase binding protein, ubiquinol-cytochrome c reductase binding protein-like, ubiquinol-cytochrome c reductase complex 14 kDa protein, ubiquinol-cytochrome c reductase, complex III subunit VI, UQBC, UQBP, UQCR6, Uqcrb, Uqcrbl, UQPC
Host Species:
Rabbit
Purification Method:
Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
362897, 67530, 7381
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles
Form:
Liquid
Applications:
Western Blot
Concentration:
2.15 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide, pH 7.3
Gene Accession No.:
P14927, Q9D855
Gene Symbols:
UQCRB
Immunogen:
Recombinant fusion protein containing a sequence corresponding to amino acids 1-111 of human UQCRB (NP_0062851)
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG
Antigen: ACE2
Classification: Polyclonal
Conjugate: Unconjugated
Gene: ACE2
Gene Alias: 2010305L05Rik, ACE 2, Ace2, ACEH, ACE-related carboxypeptidase, angiotensin I converting enzyme (peptidyl-dipeptidase A) 2, angiotensin I converting enzyme 2, angiotensin-converting enzyme 2, Angiotensin-converting enzyme homolog, anigotensin I converting enzyme 2, anigotensin-converting enzyme-related carboxypeptidase, metalloprotease MPROT15, peptidyl-dipeptidase A, Processed angiotensin-converting enzyme 2, renal angiotensin-converting enzyme 2, UNQ868/PRO1885
Host Species: Rabbit
Purification Method: Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 302668, 59272, 70008
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles
Form: Liquid
Applications: Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Concentration: 2.78 mg/mL
Formulation: PBS with 50% glycerol and 0.05% ProClin 300, pH 7.3
Gene Accession No.: Q5EGZ1, Q8R0I0, Q9BYF1
Gene Symbols: ACE2
Immunogen: A synthetic peptide corresponding to a sequence within amino acids 18-740 of human ACE2 (NP_0685761)
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human, Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
ACE2
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
ACE2
Gene Alias:
2010305L05Rik, ACE 2, Ace2, ACEH, ACE-related carboxypeptidase, angiotensin I converting enzyme (peptidyl-dipeptidase A) 2, angiotensin I converting enzyme 2, angiotensin-converting enzyme 2, Angiotensin-converting enzyme homolog, anigotensin I converting enzyme 2, anigotensin-converting enzyme-related carboxypeptidase, metalloprotease MPROT15, peptidyl-dipeptidase A, Processed angiotensin-converting enzyme 2, renal angiotensin-converting enzyme 2, UNQ868/PRO1885
Host Species:
Rabbit
Purification Method:
Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
302668, 59272, 70008
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles
Form:
Liquid
Applications:
Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Concentration:
2.78 mg/mL
Formulation:
PBS with 50% glycerol and 0.05% ProClin 300, pH 7.3
Gene Accession No.:
Q5EGZ1, Q8R0I0, Q9BYF1
Gene Symbols:
ACE2
Immunogen:
A synthetic peptide corresponding to a sequence within amino acids 18-740 of human ACE2 (NP_0685761)
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human, Mouse, Rat
Product Type:
Antibody
Isotype:
IgG
Antigen: Neuropilin 2
Classification: Polyclonal
Conjugate: Unconjugated
Gene: NRP2
Gene Alias: 1110048P06Rik, neuropilin 2, neuropilin-2, neuropilin-2a(17), neuropilin-2a(22), neuropilin-2b(0), Np2, Np-2, Npn2, Npn-2, NRP2, PRO2714, receptor for VEGF165 and semaphorins class3, vascular endothelial cell growth factor 165 receptor 2, VEGF165R2
Host Species: Rabbit
Purification Method: Affinity Chromatography
Regulatory Status: RUO
Gene ID (Entrez): 18187, 81527
Content And Storage: -20° C, Avoid Freeze/Thaw Cycles
Form: Liquid
Applications: Western Blot
Concentration: 0.12 mg/mL
Formulation: PBS with 50% glycerol and 0.01% thimerosal, pH 7.3
Gene Accession No.: O35276, O35375
Gene Symbols: NRP2
Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 443-740 of human NRP2 (NP_0038632)
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Mouse, Rat
Product Type: Antibody
Isotype: IgG
Antigen:
Neuropilin 2
Classification:
Polyclonal
Conjugate:
Unconjugated
Gene:
NRP2
Gene Alias:
1110048P06Rik, neuropilin 2, neuropilin-2, neuropilin-2a(17), neuropilin-2a(22), neuropilin-2b(0), Np2, Np-2, Npn2, Npn-2, NRP2, PRO2714, receptor for VEGF165 and semaphorins class3, vascular endothelial cell growth factor 165 receptor 2, VEGF165R2
Host Species:
Rabbit
Purification Method:
Affinity Chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
18187, 81527
Content And Storage:
-20° C, Avoid Freeze/Thaw Cycles
Form:
Liquid
Applications:
Western Blot
Concentration:
0.12 mg/mL
Formulation:
PBS with 50% glycerol and 0.01% thimerosal, pH 7.3
Gene Accession No.:
O35276, O35375
Gene Symbols:
NRP2
Immunogen:
Recombinant fusion protein containing a sequence corresponding to amino acids 443-740 of human NRP2 (NP_0038632)
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Mouse, Rat
Product Type:
Antibody
Isotype:
IgG