PIPA597830

HMBS Polyclonal Antibody, Invitrogen™

Manufacturer: Thermo Scientific

Select a Size

Pack Size SKU Availability Price
Each of 1 PIPA597830-Each-of-1 In Stock ₹ 44,705.10

PIPA597830 - Each of 1

₹ 44,705.10

In Stock

Quantity

1

Base Price: ₹ 44,705.10

GST (18%): ₹ 8,046.918

Total Price: ₹ 52,752.018

Antigen

HMBS

Classification

Polyclonal

Conjugate

Unconjugated

Gene

Hmbs

Gene Alias

alternative name: porphobilinogen deaminase, HEM3, hemC, HMBS, Hydroxymethylbilane synthase, PBG D, PBGD, PBG-D, PORC, Porphobilinogen deaminase, porphyria, acute, Chester type, pre-uroporphyrinogen synthase, similar to Porphobilinogen deaminase (Hydroxymethylbilane synthase) (HMBS) (Pre-uroporphyrinogen synthase) (PBG-D), T25658, Ups, uroporphyrinogen I synthase, uroporphyrinogen I synthetase, URO-S, Uros1

Host Species

Rabbit

Purification Method

Protein G

Regulatory Status

RUO

Gene ID (Entrez)

3145

Content And Storage

-20°C or -80°C if preferred

Form

Liquid

Applications

ELISA, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot

Concentration

5 mg/mL

Formulation

PBS with 50% glycerol and 0.03% ProClin 300, pH 7.4

Gene Accession No.

P08397

Gene Symbols

Hmbs

Immunogen

Recombinant Human Porphobilinogen deaminase protein (283-330AA)

Quantity

100 μg

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Isotype

IgG

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Description

  • PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway
  • PBGD belongs to the HMBS (hydroxymethylbilane synthase) family
  • Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP)
  • AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.

Compare Similar Items

Show Difference

Img

Thermo Scientific

PIPA597830

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Antigen:
HMBS

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
Hmbs

Gene Alias:
alternative name: porphobilinogen deaminase, HEM3, hemC, HMBS, Hydroxymethylbilane synthase, PBG D, PBGD, PBG-D, PORC, Porphobilinogen deaminase, porphyria, acute, Chester type, pre-uroporphyrinogen synthase, similar to Porphobilinogen deaminase (Hydroxymethylbilane synthase) (HMBS) (Pre-uroporphyrinogen synthase) (PBG-D), T25658, Ups, uroporphyrinogen I synthase, uroporphyrinogen I synthetase, URO-S, Uros1

Host Species:
Rabbit

Purification Method:
Protein G

Regulatory Status:
RUO

Gene ID (Entrez):
3145

Content And Storage:
-20°C or -80°C if preferred

Form:
Liquid

Applications:
ELISA, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot

Concentration:
5 mg/mL

Formulation:
PBS with 50% glycerol and 0.03% ProClin 300, pH 7.4

Gene Accession No.:
P08397

Gene Symbols:
Hmbs

Immunogen:
Recombinant Human Porphobilinogen deaminase protein (283-330AA)

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA597832

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Antigen:
hnRNP A1

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
Hnrnpa1

Gene Alias:
ALS19, ALS20, Fli-2, Hdp, HDP-1, Helix-destabilizing protein, heterogeneous nuclear ribonucleoprotein A1, Heterogeneous nuclear ribonucleoprotein A1, N-terminally processed, heterogeneous nuclear ribonucleoprotein A1B protein, heterogeneous nuclear ribonucleoprotein B2 protein, heterogeneous nuclear ribonucleoprotein core protein A1, hnRNP A1, hnRNP A1-like 3, hnRNP core protein A1, hnRNP core protein A1-like 3, hnRNP I, Hnrnpa1, hnRNP-A1, HNRNPI, HNRNP-I, Hnrpa1, HNRPA1L3, HNRPA1MGC102835, HNRPI, I79_022927, IBMPFD3, MGC102835, MGC128297 protein, nuclear ribonucleoprotein particle A1 protein, pPTB, PTB, PTB-1, PTB2, PTB3, PTB4, PTB-T, putative heterogeneous nuclear ribonucleoprotein A1-like 3, Putative heterogeneous nuclear ribonucleoprotein A1-like protein 3, ROA1, RP11-78J21.1, single-strand DNA-binding protein UP1, single-strand RNA-binding protein, Single-strand-binding protein, Tis, Topoisomerase-inhibitor suppressed, unwinding protein 1, UP 1, UP1

Host Species:
Rabbit

Purification Method:
Protein G

Regulatory Status:
RUO

Gene ID (Entrez):
3178

Content And Storage:
-20°C or -80°C if preferred

Form:
Liquid

Applications:
ELISA, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot

Concentration:
3.89 mg/mL

Formulation:
PBS with 50% glycerol and 0.03% ProClin 300, pH 7.4

Gene Accession No.:
P09651

Gene Symbols:
Hnrnpa1

Immunogen:
Recombinant Human Heterogeneous nuclear ribonucleoprotein A1 protein (2-354AA)

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA597833

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Antigen:
hnRNP AB

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
HNRNPAB

Gene Alias:
3010025C11Rik, A1F-C1, ABBP1, ABBP-1, apobec-1 binding protein 1, APOBEC1-binding protein 1, apolipoprotein B mRNA editing enzyme, catalytic polypeptide 1-binding protein 1, CArG-binding factor-A, Cbf-a, Cgbfa, Heterogeneous nuclear ribonucleoprotein A/B, hnRNP A/B, hnRNP type A/B protein, HNRNPAB, Hnrpab, S1 protein D2

Host Species:
Rabbit

Purification Method:
Protein G

Regulatory Status:
RUO

Gene ID (Entrez):
3182

Content And Storage:
-20°C or -80°C if preferred

Form:
Liquid

Applications:
ELISA, Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot

Concentration:
2.72 mg/mL

Formulation:
PBS with 50% glycerol and 0.03% ProClin 300, pH 7.4

Gene Accession No.:
Q99729

Gene Symbols:
HNRNPAB

Immunogen:
Recombinant Human Heterogeneous nuclear ribonucleoprotein A/B protein (1-68AA)

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human

Product Type:
Antibody

Isotype:
IgG

Img

Thermo Scientific

PIPA597834

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Antigen:
hnRNP L

Classification:
Polyclonal

Conjugate:
Unconjugated

Gene:
HNRNPL

Gene Alias:
C79783, D830027H13Rik, Fblim1, FLJ35509, Heterogeneous nuclear ribonucleoprotein L, heterogenous nuclear ribonucleoprotein L, hnRNP L, Hnrnpl, hnRNP-L, Hnrpl, P/OKcl.14

Host Species:
Rabbit

Purification Method:
Protein G

Regulatory Status:
RUO

Gene ID (Entrez):
15388, 3191

Content And Storage:
-20°C or -80°C if preferred

Form:
Liquid

Applications:
ELISA, Immunohistochemistry (Paraffin), Western Blot

Concentration:
4 mg/mL

Formulation:
PBS with 50% glycerol and 0.03% ProClin 300, pH 7.4

Gene Accession No.:
P14866, Q8R081

Gene Symbols:
HNRNPL

Immunogen:
Recombinant Human Heterogeneous nuclear ribonucleoprotein L protein (89-335AA)

Quantity:
100 μg

Primary or Secondary:
Primary

Target Species:
Human, Mouse

Product Type:
Antibody

Isotype:
IgG