FEMA550030
HMBS Recombinant Rabbit Monoclonal Antibody (8G12), Invitrogen™
Manufacturer: Thermo Scientific
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| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | FEMA550030-Each-of-1 | In Stock | ₹ 35,764.08 |
FEMA550030 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 35,764.08
GST (18%): ₹ 6,437.534
Total Price: ₹ 42,201.614
Antigen
HMBS
Classification
Recombinant Monoclonal
Concentration
0.67 mg/mL
Formulation
PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.
P08397
Gene Symbols
Hmbs
Immunogen
A synthesized peptide derived from human HMBS
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human
Form
Liquid
Applications
ELISA, Western Blot
Clone
8G12
Conjugate
Unconjugated
Gene
Hmbs
Gene Alias
alternative name: porphobilinogen deaminase, HEM3, hemC, HMBS, Hydroxymethylbilane synthase, PBG D, PBGD, PBG-D, PORC, Porphobilinogen deaminase, porphyria, acute, Chester type, pre-uroporphyrinogen synthase, similar to Porphobilinogen deaminase (Hydroxymethylbilane synthase) (HMBS) (Pre-uroporphyrinogen synthase) (PBG-D), T25658, Ups, uroporphyrinogen I synthase, uroporphyrinogen I synthetase, URO-S, Uros1
Host Species
Rabbit
Purification Method
Affinity chromatography
Regulatory Status
RUO
Gene ID (Entrez)
3145
Content And Storage
-20°C or -80°C if preferred
Isotype
IgG
Related Products
Description
- PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway
- PBGD belongs to the HMBS (hydroxymethylbilane synthase) family
- Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP)
- AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.
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Antigen: HMBS
Classification: Recombinant Monoclonal
Concentration: 0.67 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.: P08397
Gene Symbols: Hmbs
Immunogen: A synthesized peptide derived from human HMBS
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Form: Liquid
Applications: ELISA, Western Blot
Clone: 8G12
Conjugate: Unconjugated
Gene: Hmbs
Gene Alias: alternative name: porphobilinogen deaminase, HEM3, hemC, HMBS, Hydroxymethylbilane synthase, PBG D, PBGD, PBG-D, PORC, Porphobilinogen deaminase, porphyria, acute, Chester type, pre-uroporphyrinogen synthase, similar to Porphobilinogen deaminase (Hydroxymethylbilane synthase) (HMBS) (Pre-uroporphyrinogen synthase) (PBG-D), T25658, Ups, uroporphyrinogen I synthase, uroporphyrinogen I synthetase, URO-S, Uros1
Host Species: Rabbit
Purification Method: Affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 3145
Content And Storage: -20°C or -80°C if preferred
Isotype: IgG
Antigen:
HMBS
Classification:
Recombinant Monoclonal
Concentration:
0.67 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.:
P08397
Gene Symbols:
Hmbs
Immunogen:
A synthesized peptide derived from human HMBS
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Form:
Liquid
Applications:
ELISA, Western Blot
Clone:
8G12
Conjugate:
Unconjugated
Gene:
Hmbs
Gene Alias:
alternative name: porphobilinogen deaminase, HEM3, hemC, HMBS, Hydroxymethylbilane synthase, PBG D, PBGD, PBG-D, PORC, Porphobilinogen deaminase, porphyria, acute, Chester type, pre-uroporphyrinogen synthase, similar to Porphobilinogen deaminase (Hydroxymethylbilane synthase) (HMBS) (Pre-uroporphyrinogen synthase) (PBG-D), T25658, Ups, uroporphyrinogen I synthase, uroporphyrinogen I synthetase, URO-S, Uros1
Host Species:
Rabbit
Purification Method:
Affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
3145
Content And Storage:
-20°C or -80°C if preferred
Isotype:
IgG
Antigen: Arginase 2
Classification: Recombinant Monoclonal
Concentration: 0.6 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.: P78540
Gene Symbols: ARG2
Immunogen: A synthesized peptide derived from human ARG2
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Form: Liquid
Applications: ELISA, Flow Cytometry, Immunocytochemistry, Immunohistochemistry (Paraffin)
Clone: 9A4
Conjugate: Unconjugated
Gene: ARG2
Gene Alias: AII, AII type II arginase, ARG2, arginase 2, arginase II, arginase type II, arginase, type II, arginase-2, mitochondrial, AU022422, kidney arginase, kidney-type arginase, L-arginine amidinohydrolase, L-arginine ureahydrolase, nonhepatic arginase, non-hepatic arginase, type II arginase
Host Species: Rabbit
Purification Method: Affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 384
Content And Storage: -20°C or -80°C if preferred
Isotype: IgG
Antigen:
Arginase 2
Classification:
Recombinant Monoclonal
Concentration:
0.6 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.:
P78540
Gene Symbols:
ARG2
Immunogen:
A synthesized peptide derived from human ARG2
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Form:
Liquid
Applications:
ELISA, Flow Cytometry, Immunocytochemistry, Immunohistochemistry (Paraffin)
Clone:
9A4
Conjugate:
Unconjugated
Gene:
ARG2
Gene Alias:
AII, AII type II arginase, ARG2, arginase 2, arginase II, arginase type II, arginase, type II, arginase-2, mitochondrial, AU022422, kidney arginase, kidney-type arginase, L-arginine amidinohydrolase, L-arginine ureahydrolase, nonhepatic arginase, non-hepatic arginase, type II arginase
Host Species:
Rabbit
Purification Method:
Affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
384
Content And Storage:
-20°C or -80°C if preferred
Isotype:
IgG
Antigen: LRP2
Classification: Recombinant Monoclonal
Concentration: 3 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.: P98164
Gene Symbols: Lrp2
Immunogen: A synthesized peptide derived from human LRP2
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Form: Liquid
Applications: ELISA, Flow Cytometry
Clone: 10B5
Conjugate: Unconjugated
Gene: Lrp2
Gene Alias: AI315343, AW536255, b2b1625.2Clo, calcium sensor protein, D230004K18Rik, DBS, Glycoprotein 330, Gp330, Heymann nephritis antigen homolog, LDL receptor related protein 2, low density lipoprotein receptor-related protein 2, low density lipoprotein-related protein 2, low-density lipoprotein receptor-related protein 2, Lrp2, LRP-2, Megalin
Host Species: Rabbit
Purification Method: Affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 4036
Content And Storage: -20°C or -80°C if preferred
Isotype: IgG
Antigen:
LRP2
Classification:
Recombinant Monoclonal
Concentration:
3 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.:
P98164
Gene Symbols:
Lrp2
Immunogen:
A synthesized peptide derived from human LRP2
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Form:
Liquid
Applications:
ELISA, Flow Cytometry
Clone:
10B5
Conjugate:
Unconjugated
Gene:
Lrp2
Gene Alias:
AI315343, AW536255, b2b1625.2Clo, calcium sensor protein, D230004K18Rik, DBS, Glycoprotein 330, Gp330, Heymann nephritis antigen homolog, LDL receptor related protein 2, low density lipoprotein receptor-related protein 2, low density lipoprotein-related protein 2, low-density lipoprotein receptor-related protein 2, Lrp2, LRP-2, Megalin
Host Species:
Rabbit
Purification Method:
Affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
4036
Content And Storage:
-20°C or -80°C if preferred
Isotype:
IgG
Antigen: AHCY
Classification: Recombinant Monoclonal
Concentration: 0.33 mg/mL
Formulation: PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.: P23526
Gene Symbols: AHCY
Immunogen: A synthesized peptide derived from human AHCY
Quantity: 100 μL
Primary or Secondary: Primary
Target Species: Human
Form: Liquid
Applications: ELISA, Western Blot
Clone: 13H8
Conjugate: Unconjugated
Gene: AHCY
Gene Alias: AA987153, Acetylation, Adenosylhomocysteinase, adoHcyase, AHCY, AL024110, cb1079, CuBP, D150, dtp, ducttrip, hm:zeh1173, hm:zeh1364, Hydrolase, Liver copper-binding protein, NAD, Polymorphism, S-adenosylhomocysteine hydrolase, S-adenosyl-L-homocysteine hydrolase, SAHH, wu:fj67b02
Host Species: Rabbit
Purification Method: Affinity chromatography
Regulatory Status: RUO
Gene ID (Entrez): 191
Content And Storage: -20°C or -80°C if preferred
Isotype: IgG
Antigen:
AHCY
Classification:
Recombinant Monoclonal
Concentration:
0.33 mg/mL
Formulation:
PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.:
P23526
Gene Symbols:
AHCY
Immunogen:
A synthesized peptide derived from human AHCY
Quantity:
100 μL
Primary or Secondary:
Primary
Target Species:
Human
Form:
Liquid
Applications:
ELISA, Western Blot
Clone:
13H8
Conjugate:
Unconjugated
Gene:
AHCY
Gene Alias:
AA987153, Acetylation, Adenosylhomocysteinase, adoHcyase, AHCY, AL024110, cb1079, CuBP, D150, dtp, ducttrip, hm:zeh1173, hm:zeh1364, Hydrolase, Liver copper-binding protein, NAD, Polymorphism, S-adenosylhomocysteine hydrolase, S-adenosyl-L-homocysteine hydrolase, SAHH, wu:fj67b02
Host Species:
Rabbit
Purification Method:
Affinity chromatography
Regulatory Status:
RUO
Gene ID (Entrez):
191
Content And Storage:
-20°C or -80°C if preferred
Isotype:
IgG